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0 Congenital absence and malformations of spleen

Excludes1: isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6)

Q89.01 Asplenia (congenital)

Q89.09 Congenital malformations of spleen

Congenital splenomegaly

Q89.1 Congenital malformations of adrenal gland

Excludes1: adrenogenital disorders (E25.-)

congenital adrenal hyperplasia (E25.0)

Q89.2 Congenital malformations of other endocrine glands

Congenital malformation of parathyroid or thyroid gland

Persistent thyroglossal duct

Thyroglossal cyst

Excludes1: congenital goiter (E03.0)

congenital hypothyroidism (E03.1)

Q89.3 Situs inversus

Dextrocardia with situs inversus

Mirror-image atrial arrangement with situs inversus

Situs inversus or transversus abdominalis

Situs inversus or transversus thoracis

Transposition of abdominal viscera

Transposition of thoracic viscera

Excludes1: dextrocardia NOS (Q24.0)

Q89.4 Conjoined twins

Craniopagus

Dicephaly

Pygopagus

Thoracopagus

Q89.7 Multiple congenital malformations, not elsewhere classified

Multiple congenital anomalies NOS

Multiple congenital deformities NOS

Excludes1: congenital malformation syndromes affecting multiple systems (Q87.-)

Q89.8 Other specified congenital malformations

Use additional code(s) to identify all associated manifestations

Q89.9 Congenital malformation, unspecified

Congenital anomaly NOS

Congenital deformity NOS

Chromosomal abnormalities, not elsewhere classified (Q90-Q99)

Excludes2: mitochondrial metabolic disorders (E88.3-)

Q90 Down syndrome

Use