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D disease

Hb-E disease
Hemoglobinopathy NOS
Unstable hemoglobin hemolytic disease
Excludes1: familial polycythemia (D75.0)
Hb-M disease (D74.0)
hereditary persistence of fetal hemoglobin [HPFH] (D56.4)
high-altitude polycythemia (D75.1)
methemoglobinemia (D74.-)
D58.8 Other specified hereditary hemolytic anemias
D58.9 Hereditary hemolytic anemia, unspecified

D59 Acquired hemolytic anemia

D59.0 Drug-induced autoimmune hemolytic anemia
Code first (T36-T50) to identify drug
D59.1 Other autoimmune hemolytic anemias
Autoimmune hemolytic disease (cold type) (warm type)
Chronic cold hemagglutinin disease
Cold agglutinin disease
Cold agglutinin hemoglobinuria
Cold type (secondary) (symptomatic) hemolytic anemia
Warm type (secondary) (symptomatic) hemolytic anemia
Excludes1: Evans syndrome (D69.41)
hemolytic disease of newborn (P55.-)
paroxysmal cold hemoglobinuria (D59.6)
D59.2 Drug-induced nonautoimmune hemolytic anemia
Drug-induced enzyme deficiency anemia
Code first (T36-T50) to identify drug
D59.3 Hemolytic-uremic syndrome
D59.4 Other nonautoimmune hemolytic anemias
Mechanical hemolytic anemia
Microangiopathic hemolytic anemia
Toxic hemolytic anemia
D59.5 Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]
Excludes1: hemoglobinuria NOS (R82.3)
D59.6 Hemoglobinuria due to hemolysis from other external causes
Hemoglobinuria from exertion
March hemoglobinuria
Paroxysmal cold hemoglobinuria
Use additional code (Chapter 20) to identify external cause
Excludes1: hemoglobinuria NOS (R82.3)
D59.8 Other acquired hemolytic anemias
D59.9 Acquired hemolytic anemia, unspecified
Idiopathic hemolytic anemia, chronic

=Aplastic