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recessive agammaglobulinemia (Swiss type)

X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)

D80.1 Nonfamilial hypogammaglobulinemia

Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes

Common variable agammaglobulinemia [CVAgamma]

Hypogammaglobulinemia NOS

D80.2 Selective deficiency of immunoglobulin A [IgA]

D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses

D80.4 Selective deficiency of immunoglobulin M [IgM]

D80.5 Immunodeficiency with increased immunoglobulin M [IgM]

D80.6 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia

D80.7 Transient hypogammaglobulinemia of infancy

D80.8 Other immunodeficiencies with predominantly antibody defects

Kappa light chain deficiency

D80.9 Immunodeficiency with predominantly antibody defects, unspecified

D81 Combined immunodeficiencies

Excludes1: autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis

D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers

D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers

D81.3 Adenosine deaminase [ADA] deficiency

D81.4 Nezelof's syndrome

D81.5 Purine nucleoside phosphorylase [PNP] deficiency

D81.6 Major histocompatibility complex class I deficiency

Bare lymphocyte syndrome

D81.7 Major histocompatibility complex class II deficiency

D81.8 Other combined immunodeficiencies

D81.81 Biotin-dependent carboxylase deficiency

Multiple carboxylase deficiency

Excludes1: biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

D81.810 Biotinidase deficiency

D81.818 Other biotin-dependent carboxylase deficiency

Holocarboxylase synthetase deficiency

Other multiple carboxylase deficiency

D81.819 Biotin-dependent carboxylase deficiency, unspecified

Multiple carboxylase deficiency, unspecified

D81.