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type IVB
- E76.219 Morquio mucopolysaccharidoses, unspecified
- Morquio syndrome
- Mucopolysaccharidosis, type IV
- E76.219 Morquio mucopolysaccharidoses, unspecified
- E76.22 Sanfilippo mucopolysaccharidoses
- Mucopolysaccharidosis, type III (A) (B) (C) (D)
- Sanfilippo A syndrome
- Sanfilippo B syndrome
- Sanfilippo C syndrome
- Sanfilippo D syndrome
- E76.29 Other mucopolysaccharidoses
- beta-Glucuronidase deficiency
- Maroteaux-Lamy (mild) (severe) syndrome
- Mucopolysaccharidosis, types VI, VII
- E76.3 Mucopolysaccharidosis, unspecified
- E76.8 Other disorders of glucosaminoglycan metabolism
- E76.9 Glucosaminoglycan metabolism disorder, unspecified
E77 Disorders of glycoprotein metabolism
- E77.0 Defects in post-translational modification of lysosomal enzymes
- Mucolipidosis II [I-cell disease]
- Mucolipidosis III [pseudo-Hurler polydystrophy]
- E77.1 Defects in glycoprotein degradation
- Aspartylglucosaminuria
- Fucosidosis
- Mannosidosis
- Sialidosis [mucolipidosis I]
- E77.8 Other disorders of glycoprotein metabolism
- E77.9 Disorder of glycoprotein metabolism, unspecified
- E78 Disorders of lipoprotein metabolism and other lipidemias
- Excludes1: sphingolipidosis (E75.0-E75.3)
E78.0 Pure hypercholesterolemia
- Familial hypercholesterolemia
- Fredrickson's hyperlipoproteinemia, type IIa
- Hyperbetalipoproteinemia
- Hyperlipidemia, Group A
- Low-density-lipoprotein-type [LDL] hyperlipoproteinemia
- E78.1 Pure hyperglyceridemia
- Elevated fasting triglycerides
- Endogenous hyperglyceridemia
- Fredrickson's hyperlipoproteinemia, type IV
- Hyperlipidemia, group B
- Hyperprebetalipoproteinemia
- Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia
- E78.