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dementia with behavioral disturbance (F02.81)
dementia without behavioral disturbance (F02.80)
A81.0 Creutzfeldt-Jakob disease
A81.00 Creutzfeldt-Jakob disease, unspecified
Jakob-Creutzfeldt disease, unspecified
A81.01 Variant Creutzfeldt-Jakob disease
vCJD
A81.09 Other Creutzfeldt-Jakob disease
CJD
Familial Creutzfeldt-Jakob disease
Iatrogenic Creutzfeldt-Jakob disease
Sporadic Creutzfeldt-Jakob disease
Subacute spongiform encephalopathy (with dementia)
A81.1 Subacute sclerosing panencephalitis
Dawson's inclusion body encephalitis
Van Bogaert's sclerosing leukoencephalopathy
A81.2 Progressive multifocal leukoencephalopathy
Multifocal leukoencephalopathy NOS
A81.8 Other atypical virus infections of central nervous system
A81.81 Kuru
A81.82 Gerstmann-Sträussler-Scheinker syndrome
GSS syndrome
A81.83 Fatal familial insomnia
FFI
A81.89 Other atypical virus infections of central nervous system
A81.9 Atypical virus infection of central nervous system, unspecified
Prion diseases of the central nervous system NOS

A82 Rabies

A82.0 Sylvatic rabies
A82.1 Urban rabies
A82.9 Rabies, unspecified

A83 Mosquito-borne viral encephalitis

Includes: mosquito-borne viral meningoencephalitis
Excludes2: Venezuelan equine encephalitis (A92.2)
West Nile fever (A92.3-)
West Nile virus (A92.3-)
A83.0 Japanese encephalitis
A83.1 Western equine encephalitis
A83.2 Eastern equine encephalitis
A83.3 St Louis encephalitis
A83.4 Australian encephalitis
Kunjin virus disease
A83.5 California encephalitis
California meningoencephalitis