Endocrine, nutritional and metabolic diseases (E00-E90)
edit- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
- Excludes1: transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- This chapter contains the following blocks:
- E00-E07 Disorders of thyroid gland
- E08-E13 Diabetes mellitus
- E15-E16 Other disorders of glucose regulation and pancreatic internal secretion
- E20-E35 Disorders of other endocrine glands
- E36 Intraoperative complications of endocrine system
- E40-E46 Malnutrition
- E50-E64 Other nutritional deficiencies
- E65-E68 Overweight, obesity and other hyperalimentation
- E70-E88 Metabolic disorders
- E89 Postprocedural endocrine and metabolic complications and disorders, not elsewhere classified
Disorders of thyroid gland (E00-E07)
editE00 Congenital iodine-deficiency syndrome
edit- Use additional code (F70-F79) to identify associated mental retardation.
- Excludes1: subclinical iodine-deficiency hypothyroidism (E02)
- E00.0 Congenital iodine-deficiency syndrome, neurological type
- Endemic cretinism, neurological type
- E00.1 Congenital iodine-deficiency syndrome, myxedematous type
- Endemic hypothyroid cretinism
- Endemic cretinism, myxedematous type
- E00.2 Congenital iodine-deficiency syndrome, mixed type
- Endemic cretinism, mixed type
- E00.9 Congenital iodine-deficiency syndrome, unspecified
- Congenital iodine-deficiency hypothyroidism NOS
- Endemic cretinism NOS
E01 Iodine-deficiency related thyroid disorders and allied conditions
edit- Excludes1: congenital iodine-deficiency syndrome (E00.-)
- subclinical iodine-deficiency hypothyroidism (E02)
- E01.0 Iodine-deficiency related diffuse (endemic) goiter
- E01.1 Iodine-deficiency related multinodular (endemic) goiter
- Iodine-deficiency related nodular goiter
- E01.2 Iodine-deficiency related (endemic) goiter, unspecified
- Endemic goiter NOS
- E01.8 Other iodine-deficiency related thyroid disorders and allied conditions
- Acquired iodine-deficiency hypothyroidism NOS
E02 Subclinical iodine-deficiency hypothyroidism
editE03 Other hypothyroidism
edit- Excludes1: iodine-deficiency related hypothyroidism (E00-E02)
- postprocedural hypothyroidism (E89.0)
- E03.0 Congenital hypothyroidism with diffuse goiter
- Congenital parenchymatous goiter (nontoxic)
- Congenital goiter (nontoxic) NOS
- Excludes1: transitory congenital goiter with normal function (P72.0)
- E03.1 Congenital hypothyroidism without goiter
- Aplasia of thyroid (with myxedema)
- Congenital atrophy of thyroid
- Congenital hypothyroidism NOS
- E03.2 Hypothyroidism due to medicaments and other exogenous substances
- Code first (T36-T65) to identify drug or substance
- E03.3 Postinfectious hypothyroidism
- E03.4 Atrophy of thyroid (acquired)
- Excludes1: congenital atrophy of thyroid (E03.1)
- E03.5 Myxedema coma
- E03.8 Other specified hypothyroidism
- E03.9 Hypothyroidism, unspecified
- Myxedema NOS
E04 Other nontoxic goiter
edit- Excludes1: congenital goiter (NOS) (diffuse) (parenchymatous) (E03.0)
- iodine-deficiency related goiter (E00-E02)
- E04.0 Nontoxic diffuse goiter
- Diffuse ( colloid) nontoxic goiter
- Simple nontoxic goiter
- E04.1 Nontoxic single thyroid nodule
- Colloid nodule (cystic) (thyroid)
- Nontoxic uninodular goiter
- Thyroid (cystic) nodule NOS
- E04.2 Nontoxic multinodular goiter
- Cystic goiter NOS
- Multinodular (cystic) goiter NOS
- E04.8 Other specified nontoxic goiter
- E04.9 Nontoxic goiter, unspecified
- Goiter NOS
- Nodular goiter (nontoxic) NOS
E05 Thyrotoxicosis [hyperthyroidism]
edit- Excludes1: chronic thyroiditis with transient thyrotoxicosis (E06.2)
- neonatal thyrotoxicosis (P72.1)
- E05.0 Thyrotoxicosis with diffuse goiter
- Exophthalmic or toxic goiter NOS
- Graves' disease
- Toxic diffuse goiter
- E05.00 Thyrotoxicosis with diffuse goiter without thyrotoxic crisis or storm
- E05.01 Thyrotoxicosis with diffuse goiter with thyrotoxic crisis or storm
- E05.1 Thyrotoxicosis with toxic single thyroid nodule
- Thyrotoxicosis with toxic uninodular goiter
- E05.10 Thyrotoxicosis with toxic single thyroid nodule without thyrotoxic crisis or storm
- E05.11 Thyrotoxicosis with toxic single thyroid nodule with thyrotoxic crisis or storm
- E05.2 Thyrotoxicosis with toxic multinodular goiter
- Toxic nodular goiter NOS
- E05.20 Thyrotoxicosis with toxic multinodular goiter without thyrotoxic crisis or storm
- E05.21 Thyrotoxicosis with toxic multinodular goiter with thyrotoxic crisis or storm
- E05.3 Thyrotoxicosis from ectopic thyroid tissue
- E05.30 Thyrotoxicosis from ectopic thyroid tissue without thyrotoxic crisis or storm
- E05.31 Thyrotoxicosis from ectopic thyroid tissue with thyrotoxic crisis or storm
- E05.4 Thyrotoxicosis factitia
- E05.40 Thyrotoxicosis factitia without thyrotoxic crisis or storm
- E05.41 Thyrotoxicosis factitia with thyrotoxic crisis or storm
- E05.8 Other thyrotoxicosis
- Overproduction of thyroid-stimulating hormone
- E05.80 Other thyrotoxicosis without thyrotoxic crisis or storm
- E05.81 Other thyrotoxicosis with thyrotoxic crisis or storm
- E05.9 Thyrotoxicosis, unspecified
- Hyperthyroidism NOS
- E05.90 Thyrotoxicosis, unspecified without thyrotoxic crisis or storm
- E05.91 Thyrotoxicosis, unspecified with thyrotoxic crisis or storm
E06 Thyroiditis
edit- Excludes1: postpartum thyroiditis (O90.5)
- E06.0 Acute thyroiditis
- Abscess of thyroid
- Pyogenic thyroiditis
- Suppurative thyroiditis
- Use additional code (B95-B97) to identify infectious agent.
- E06.1 Subacute thyroiditis
- de Quervain thyroiditis
- Giant-cell thyroiditis
- Granulomatous thyroiditis
- Nonsuppurative thyroiditis
- Viral thyroiditis
- Excludes1: autoimmune thyroiditis (E06.3)
- E06.2 Chronic thyroiditis with transient thyrotoxicosis
- Excludes1: autoimmune thyroiditis (E06.3)
- E06.3 Autoimmune thyroiditis
- Hashimoto's thyroiditis
- Hashitoxicosis (transient)
- Lymphadenoid goiter
- Lymphocytic thyroiditis
- Struma lymphomatosa
- E06.4 Drug-induced thyroiditis
- Code first (T36-T50) to identify drug
- E06.5 Other chronic thyroiditis
- Chronic fibrous thyroiditis
- Chronic thyroiditis NOS
- Ligneous thyroiditis
- Riedel thyroiditis
- E06.9 Thyroiditis, unspecified
E07 Other disorders of thyroid
edit- E07.0 Hypersecretion of calcitonin
- C-cell hyperplasia of thyroid
- Hypersecretion of thyrocalcitonin
- E07.1 Dyshormogenetic goiter
- Familial dyshormogenetic goiter
- Pendred' s syndrome
- Excludes1: transitory congenital goiter with normal function (P72.0)
- E07.8 Other specified disorders of thyroid
- E07.81 Sick-euthyroid syndrome
- Euthyroid sick-syndrome
- E07.89 Other specified disorders of thyroid
- Abnormality of thyroid-binding globulin
- Hemorrhage of thyroid
- Infarction of thyroid
- E07.81 Sick-euthyroid syndrome
- E07.9 Disorder of thyroid, unspecified
Diabetes mellitus (E08-E13)
editE08 Diabetes mellitus due to underlying condition
edit- Code first the underlying condition, such as:
- Congenital rubella (P35.0)
- Cushing's syndrome (E24.-)
- Cystic fibrosis (E84.-)
- Malignant neoplasm (C00-C96)
- Malnutrition (E40-E46)
- Pancreatitis and other diseases of the pancreas (K85-K86.-)
- Use additional code to identify any insulin use (Z79.4)
- Excludes1: drug or chemical induced diabetes mellitus (E09.-)
- gestational diabetes (O24.4-)
- neonatal diabetes mellitus (P70.2)
- type 1 diabetes mellitus (E10.-)
- type 2 diabetes mellitus (E11.-)
- E08.0 Diabetes mellitus due to underlying condition with hyperosmolarity
- E08.00 Diabetes mellitus due to underlying condition with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC)
- E08.01 Diabetes mellitus due to underlying condition with hyperosmolarity with coma
- E08.1 Diabetes mellitus due to underlying condition with ketoacidosis
- E08.10 Diabetes mellitus due to underlying condition with ketoacidosis without coma
- E08.11 Diabetes mellitus due to underlying condition with ketoacidosis with coma
- E08.2 Diabetes mellitus due to underlying condition with kidney complications
- E08.21 Diabetes mellitus due to underlying condition with diabetic nephropathy
- Diabetes mellitus due to underlying condition with intercapillary glomerulosclerosis
- Diabetes mellitus due to underlying condition with intracapillary glomerulonephrosis
- Diabetes mellitus due to underlying condition with Kimmelstiel-Wilson disease
- E08.22 Diabetes mellitus due to underlying condition with diabetic chronic kidney disease
- Diabetes mellitus due to underlying condition with chronic kidney disease due to conditions classified to .21 and .22
- Use additional code to identify stage of chronic kidney disease (N18.1-N18.6)
- E08.29 Diabetes mellitus due to underlying condition with other diabetic kidney complication
- Renal tubular degeneration in diabetes mellitus due to underlying condition
- E08.21 Diabetes mellitus due to underlying condition with diabetic nephropathy
- E08.3 Diabetes mellitus due to underlying condition with ophthalmic complications
- E08.31 Diabetes mellitus due to underlying condition with unspecified diabetic retinopathy
- E08.311 Diabetes mellitus due to underlying condition with unspecified diabetic retinopathy with macular edema
- E08.319 Diabetes mellitus due to underlying condition with unspecified diabetic retinopathy without macular edema
- E08.32 Diabetes mellitus due to underlying condition with mild nonproliferative diabetic retinopathy
- Diabetes mellitus due to underlying condition with nonproliferative diabetic retinopathy NOS
- E08.321 Diabetes mellitus due to underlying condition with mild nonproliferative diabetic retinopathy with macular edema
- E08.329 Diabetes mellitus due to underlying condition with mild nonproliferative diabetic retinopathy without macular edema
- E08.33 Diabetes mellitus due to underlying condition with moderate nonproliferative diabetic retinopathy
- E08.331 Diabetes mellitus due to underlying condition with moderate nonproliferative diabetic retinopathy with macular edema
- E08. 339 Diabetes mellitus due to underlying condition with moderate nonproliferative diabetic retinopathy without macular edema
- E08.34 Diabetes mellitus due to underlying condition with severe nonproliferative diabetic retinopathy
- E08.341 Diabetes mellitus due to underlying condition with severe nonproliferative diabetic retinopathy with macular edema
- E08.349 Diabetes mellitus due to underlying condition with severe nonproliferative diabetic retinopathy without macular edema
- E08.35 Diabetes mellitus due to underlying condition with proliferative diabetic retinopathy
- E08.351 Diabetes mellitus due to underlying condition with proliferative diabetic retinopathy with macular edema
- E08.359 Diabetes mellitus due to underlying condition with proliferative diabetic retinopathy without macular edema
- E08.36 Diabetes mellitus due to underlying condition with diabetic cataract
- E08.39 Diabetes mellitus due to underlying condition with other diabetic ophthalmic complication
- E08.31 Diabetes mellitus due to underlying condition with unspecified diabetic retinopathy
- E08.4 Diabetes mellitus due to underlying condition with neurological complications
- E08.40 Diabetes mellitus due to underlying condition with diabetic neuropathy, unspecified
- E08.41 Diabetes mellitus due to underlying condition with diabetic mononeuropathy
- E08.42 Diabetes mellitus due to underlying condition with diabetic polyneuropathy
- Diabetes mellitus due to underlying condition with diabetic neuralgia
- E08.43 Diabetes mellitus due to underlying condition with diabetic autonomic (poly)neuropathy
- Diabetes mellitus due to underlying condition with diabetic gastroparesis
- E08.44 Diabetes mellitus due to underlying condition with diabetic amyotrophy
- E08.49 Diabetes mellitus due to underlying condition with other diabetic neurological complication
- E08.5 Diabetes mellitus due to underlying condition with circulatory complications
- E08.51 Diabetes mellitus due to underlying condition with diabetic peripheral angiopathy without gangrene
- E08. 52 Diabetes mellitus due to underlying condition with diabetic peripheral angiopathy with gangrene
- Diabetes mellitus due to underlying condition with diabetic gangrene
- E08.59 Diabetes mellitus due to underlying condition with other circulatory complications
- E08.6 Diabetes mellitus due to underlying condition with other specified complications
- E08.61 Diabetes mellitus due to underlying condition with diabetic arthropathy
- E08.610 Diabetes mellitus due to underlying condition with diabetic neuropathic arthropathy
- Diabetes mellitus due to underlying condition with Charcot's joints
- E08.618 Diabetes mellitus due to underlying condition with other diabetic arthropathy
- E08.610 Diabetes mellitus due to underlying condition with diabetic neuropathic arthropathy
- E08.62 Diabetes mellitus due to underlying condition with skin complications
- E08.620 Diabetes mellitus due to underlying condition with diabetic dermatitis
- Diabetes mellitus due to underlying condition with diabetic necrobiosis lipoidica
- E08.621 Diabetes mellitus due to underlying condition with foot ulcer
- Use additional code to identify site of ulcer (L97.4-, L97.5-)
- E08.622 Diabetes mellitus due to underlying condition with other skin ulcer
- Use additional code to identify site of ulcer (L97.1-L97.9, L98.41-L98.49)
- E08.628 Diabetes mellitus due to underlying condition with other skin complications
- E08.620 Diabetes mellitus due to underlying condition with diabetic dermatitis
- E08.63 Diabetes mellitus due to underlying condition with oral complications
- E08.630 Diabetes mellitus due to underlying condition with periodontal disease
- E08.638 Diabetes mellitus due to underlying condition with other oral complications
- E08.64 Diabetes mellitus due to underlying condition with hypoglycemia
- E08.641 Diabetes mellitus due to underlying condition with hypoglycemia with coma
- E08.649 Diabetes mellitus due to underlying condition with hypoglycemia without coma
- E08. 65 Diabetes mellitus due to underlying condition with hyperglycemia
- E08.69 Diabetes mellitus due to underlying condition with other specified complication
- Use additional code to identify complication
- E08.61 Diabetes mellitus due to underlying condition with diabetic arthropathy
- E08.8 Diabetes mellitus due to underlying condition with unspecified complications
- E08.9 Diabetes mellitus due to underlying condition without complications
E09 Drug or chemical induced diabetes mellitus
edit- Code first (T36-T65) to identify drug or chemical
- Use additional code to identify any insulin use (Z79.4)
- Excludes1: diabetes mellitus due to underlying condition (E08.-)
- gestational diabetes (O24.4-)
- neonatal diabetes mellitus (P70.2)
- type 1 diabetes mellitus (E10.-)
- type 2 diabetes mellitus (E11.-)
- E09.0 Drug or chemical induced diabetes mellitus with hyperosmolarity
- E09.00 Drug or chemical induced diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC)
- E09.01 Drug or chemical induced diabetes mellitus with hyperosmolarity with coma
- E09.1 Drug or chemical induced diabetes mellitus with ketoacidosis
- E09.10 Drug or chemical induced diabetes mellitus with ketoacidosis without coma
- E09.11 Drug or chemical induced diabetes mellitus with ketoacidosis with coma
- E09.2 Drug or chemical induced diabetes mellitus with kidney complications
- E09.21 Drug or chemical induced diabetes mellitus with diabetic nephropathy
- Drug or chemical induced diabetes mellitus with intercapillary glomerulosclerosis
- Drug or chemical induced diabetes mellitus with intracapillary glomerulonephrosis
- Drug or chemical induced diabetes mellitus with Kimmelstiel-Wilson disease
- E09.22 Drug or chemical induced diabetes mellitus with diabetic chronic kidney disease
- Drug or chemical induced diabetes mellitus with chronic kidney disease due to conditions classified to .21 and .22
- Use additional code to identify stage of chronic kidney disease (N18.1-N18.6)
- E09. 29 Drug or chemical induced diabetes mellitus with other diabetic kidney complication
- Drug or chemical induced diabetes mellitus with renal tubular degeneration
- E09.21 Drug or chemical induced diabetes mellitus with diabetic nephropathy
- E09.3 Drug or chemical induced diabetes mellitus with ophthalmic complications
- E09.31 Drug or chemical induced diabetes mellitus with unspecified diabetic retinopathy
- E09.311 Drug or chemical induced diabetes mellitus with unspecified diabetic retinopathy with macular edema
- E09.319 Drug or chemical induced diabetes mellitus with unspecified diabetic retinopathy without macular edema
- E09.32 Drug or chemical induced diabetes mellitus with mild nonproliferative diabetic retinopathy
- Drug or chemical induced diabetes mellitus with nonproliferative diabetic retinopathy NOS
- E09.321 Drug or chemical induced diabetes mellitus with mild nonproliferative diabetic retinopathy with macular edema
- E09.329 Drug or chemical induced diabetes mellitus with mild nonproliferative diabetic retinopathy without macular edema
- E09.33 Drug or chemical induced diabetes mellitus with moderate nonproliferative diabetic retinopathy
- E09.331 Drug or chemical induced diabetes mellitus with moderate nonproliferative diabetic retinopathy with macular edema
- E09.339 Drug or chemical induced diabetes mellitus with moderate nonproliferative diabetic retinopathy without macular edema
- E09.34 Drug or chemical induced diabetes mellitus with severe nonproliferative diabetic retinopathy
- E09.341 Drug or chemical induced diabetes mellitus with severe nonproliferative diabetic retinopathy with macular edema
- E09.349 Drug or chemical induced diabetes mellitus with severe nonproliferative diabetic retinopathy without macular edema
- E09.35 Drug or chemical induced diabetes mellitus with proliferative diabetic retinopathy
- E09.351 Drug or chemical induced diabetes mellitus with proliferative diabetic retinopathy with macular edema
- E09. 359 Drug or chemical induced diabetes mellitus with proliferative diabetic retinopathy without macular edema
- E09.36 Drug or chemical induced diabetes mellitus with diabetic cataract
- E09.39 Drug or chemical induced diabetes mellitus with other diabetic ophthalmic complication
- E09.31 Drug or chemical induced diabetes mellitus with unspecified diabetic retinopathy
- E09.4 Drug or chemical induced diabetes mellitus with neurological complications
- E09.40 Drug or chemical induced diabetes mellitus with neurological complications with diabetic neuropathy, unspecified
- E09.41 Drug or chemical induced diabetes mellitus with neurological complications with diabetic mononeuropathy
- E09.42 Drug or chemical induced diabetes mellitus with neurological complications with diabetic polyneuropathy
- Drug or chemical induced diabetes mellitus with diabetic neuralgia
- E09.43 Drug or chemical induced diabetes mellitus with neurological complications with diabetic autonomic (poly)neuropathy
- Drug or chemical induced diabetes mellitus with diabetic gastroparesis
- E09.44 Drug or chemical induced diabetes mellitus with neurological complications with diabetic amyotrophy
- E09.49 Drug or chemical induced diabetes mellitus with neurological complications with other diabetic neurological complication
- E09.5 Drug or chemical induced diabetes mellitus with circulatory complications
- E09.51 Drug or chemical induced diabetes mellitus with diabetic peripheral angiopathy without gangrene
- E09.52 Drug or chemical induced diabetes mellitus with diabetic peripheral angiopathy with gangrene
- Drug or chemical induced diabetes mellitus with diabetic gangrene
- E09.59 Drug or chemical induced diabetes mellitus with other circulatory complications
- E09.6 Drug or chemical induced diabetes mellitus with other specified complications
- E09.61 Drug or chemical induced diabetes mellitus with diabetic arthropathy
- E09.610 Drug or chemical induced diabetes mellitus with diabetic neuropathic arthropathy
- Drug or chemical induced diabetes mellitus with Charcot's joints
- E09.618 Drug or chemical induced diabetes mellitus with other diabetic arthropathy
- E09.610 Drug or chemical induced diabetes mellitus with diabetic neuropathic arthropathy
- E09.62 Drug or chemical induced diabetes mellitus with skin complications
- E09.620 Drug or chemical induced diabetes mellitus with diabetic dermatitis
- Drug or chemical induced diabetes mellitus with diabetic necrobiosis lipoidica
- E09.621 Drug or chemical induced diabetes mellitus with foot ulcer
- Use additional code to identify site of ulcer (L97.4-, L97.5-)
- E09.622 Drug or chemical induced diabetes mellitus with other skin ulcer
- Use additional code to identify site of ulcer (L97.1-L97.9, L98.41-L98.49)
- E09.628 Drug or chemical induced diabetes mellitus with other skin complications
- E09.620 Drug or chemical induced diabetes mellitus with diabetic dermatitis
- E09.63 Drug or chemical induced diabetes mellitus with oral complications
- E09.630 Drug or chemical induced diabetes mellitus with periodontal disease
- E09.638 Drug or chemical induced diabetes mellitus with other oral complications
- E09.64 Drug or chemical induced diabetes mellitus with hypoglycemia
- E09.641 Drug or chemical induced diabetes mellitus with hypoglycemia with coma
- E09.649 Drug or chemical induced diabetes mellitus with hypoglycemia without coma
- E09.65 Drug or chemical induced diabetes mellitus with hyperglycemia
- E09.69 Drug or chemical induced diabetes mellitus with other specified complication
- Use additional code to identify complication
- E09.61 Drug or chemical induced diabetes mellitus with diabetic arthropathy
- E09.8 Drug or chemical induced diabetes mellitus with unspecified complications
- E09.9 Drug or chemical induced diabetes mellitus without complications
E10 Type 1 diabetes mellitus
edit- Includes: brittle diabetes (mellitus)
- diabetes (mellitus) due to autoimmune process
- diabetes (mellitus) due to immune mediated pancreatic islet beta-cell destruction
- idiopathic diabetes (mellitus)
- juvenile onset diabetes (mellitus)
- ketosis-prone diabetes (mellitus)
- Excludes1: diabetes mellitus due to underlying condition (E08.-)
- drug or chemical induced diabetes mellitus (E09.-)
- gestational diabetes (O24.4-)
- hyperglycemia NOS (R73.9)
- neonatal diabetes mellitus (P70.2)
- type 2 diabetes mellitus (E11.-)
- E10.1 Type 1 diabetes mellitus with ketoacidosis
- E10.10 Type 1 diabetes mellitus with ketoacidosis without coma
- E10.11 Type 1 diabetes mellitus with ketoacidosis with coma
- E10.2 Type 1 diabetes mellitus with kidney complications
- E10.21 Type 1 diabetes mellitus with diabetic nephropathy
- Type 1 diabetes mellitus with intercapillary glomerulosclerosis
- Type 1 diabetes mellitus with intracapillary glomerulonephrosis
- Type 1 diabetes mellitus with Kimmelstiel-Wilson disease
- E10.22 Type 1 diabetes mellitus with diabetic chronic kidney disease
- Type 1 diabetes mellitus with chronic kidney disease due to conditions classified to .21 and .22
- Use additional code to identify stage of chronic kidney disease (N18.1-N18.6)
- E10.29 Type 1 diabetes mellitus with other diabetic kidney complication
- Type 1 diabetes mellitus with renal tubular degeneration
- E10.21 Type 1 diabetes mellitus with diabetic nephropathy
- E10.3 Type 1 diabetes mellitus with ophthalmic complications
- E10.31 Type 1 diabetes mellitus with unspecified diabetic retinopathy
- E10.311 Type 1 diabetes mellitus with unspecified diabetic retinopathy with macular edema
- E10.319 Type 1 diabetes mellitus with unspecified diabetic retinopathy without macular edema
- E10.32 Type 1 diabetes mellitus with mild nonproliferative diabetic retinopathy
- Type 1 diabetes mellitus with nonproliferative diabetic retinopathy NOS
- E10.321 Type 1 diabetes mellitus with mild nonproliferative diabetic retinopathy with macular edema
- E10.329 Type 1 diabetes mellitus with mild nonproliferative diabetic retinopathy without macular edema
- E10. 33 Type 1 diabetes mellitus with moderate nonproliferative diabetic retinopathy
- E10.331 Type 1 diabetes mellitus with moderate nonproliferative diabetic retinopathy with macular edema
- E10.339 Type 1 diabetes mellitus with moderate nonproliferative diabetic retinopathy without macular edema
- E10.34 Type 1 diabetes mellitus with severe nonproliferative diabetic retinopathy
- E10.341 Type 1 diabetes mellitus with severe nonproliferative diabetic retinopathy with macular edema
- E10.349 Type 1 diabetes mellitus with severe nonproliferative diabetic retinopathy without macular edema
- E10.35 Type 1 diabetes mellitus with proliferative diabetic retinopathy
- E10.351 Type 1 diabetes mellitus with proliferative diabetic retinopathy with macular edema
- E10.359 Type 1 diabetes mellitus with proliferative diabetic retinopathy without macular edema
- E10.36 Type 1 diabetes mellitus with diabetic cataract
- E10.39 Type 1 diabetes mellitus with other diabetic ophthalmic complication
- E10.31 Type 1 diabetes mellitus with unspecified diabetic retinopathy
- E10.4 Type 1 diabetes mellitus with neurological complications
- E10.40 Type 1 diabetes mellitus with diabetic neuropathy, unspecified
- E10.41 Type 1 diabetes mellitus with diabetic mononeuropathy
- E10.42 Type 1 diabetes mellitus with diabetic polyneuropathy
- Type 1 diabetes mellitus with diabetic neuralgia
- E10.43 Type 1 diabetes mellitus with diabetic autonomic (poly)neuropathy
- Type 1 diabetes mellitus with diabetic gastroparesis
- E10.44 Type 1 diabetes mellitus with diabetic amyotrophy
- E10.49 Type 1 diabetes mellitus with other diabetic neurological complication
- E10.5 Type 1 diabetes mellitus with circulatory complications
- E10.51 Type 1 diabetes mellitus with diabetic peripheral angiopathy without gangrene
- E10.52 Type 1 diabetes mellitus with diabetic peripheral angiopathy with gangrene
- Type 1 diabetes mellitus with diabetic gangrene
- E10.59 Type 1 diabetes mellitus with other circulatory complications
- E10. 6 Type 1 diabetes mellitus with other specified complications
- E10.61 Type 1 diabetes mellitus with diabetic arthropathy
- E10.610 Type 1 diabetes mellitus with diabetic neuropathic arthropathy
- Type 1 diabetes mellitus with Charcot's joints
- E10.618 Type 1 diabetes mellitus with other diabetic arthropathy
- E10.610 Type 1 diabetes mellitus with diabetic neuropathic arthropathy
- E10.62 Type 1 diabetes mellitus with skin complications
- E10.620 Type 1 diabetes mellitus with diabetic dermatitis
- Type 1 diabetes mellitus with diabetic necrobiosis lipoidica
- E10.621 Type 1 diabetes mellitus with foot ulcer
- Use additional code to identify site of ulcer (L97.4-, L97.5-)
- E10.622 Type 1 diabetes mellitus with other skin ulcer
- Use additional code to identify site of ulcer (L97.1-L97.9, L98.41-L98.49)
- E10.628 Type 1 diabetes mellitus with other skin complications
- E10.620 Type 1 diabetes mellitus with diabetic dermatitis
- E10.63 Type 1 diabetes mellitus with oral complications
- E10.630 Type 1 diabetes mellitus with periodontal disease
- E10.638 Type 1 diabetes mellitus with other oral complications
- E10.64 Type 1 diabetes mellitus with hypoglycemia
- E10.641 Type 1 diabetes mellitus with hypoglycemia with coma
- E10.649 Type 1 diabetes mellitus with hypoglycemia without coma
- E10.65 Type 1 diabetes mellitus with hyperglycemia
- E10.69 Type 1 diabetes mellitus with other specified complication
- Use additional code to identify complication
- E10.61 Type 1 diabetes mellitus with diabetic arthropathy
- E10.8 Type 1 diabetes mellitus with unspecified complications
- E10.9 Type 1 diabetes mellitus without complications
E11 Type 2 diabetes mellitus
edit- Includes: diabetes (mellitus) due to insulin secretory defect
- diabetes NOS
- insulin resistant diabetes (mellitus)
- Use additional code to identify any insulin use (Z79.4)
- Excludes1: diabetes mellitus due to underlying condition (E08.-)
- drug or chemical induced diabetes mellitus (E09.-)
- gestational diabetes (O24.4-)
- neonatal diabetes mellitus (P70.2)
- type 1 diabetes mellitus (E10.-)
- E11.0 Type 2 diabetes mellitus with hyperosmolarity
- E11.00 Type 2 diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC)
- E11.01 Type 2 diabetes mellitus with hyperosmolarity with coma
- E11.2 Type 2 diabetes mellitus with kidney complications
- E11.21 Type 2 diabetes mellitus with diabetic nephropathy
- Type 2 diabetes mellitus with intercapillary glomerulosclerosis
- Type 2 diabetes mellitus with intracapillary glomerulonephrosis
- Type 2 diabetes mellitus with Kimmelstiel-Wilson disease
- E11.22 Type 2 diabetes mellitus with diabetic chronic kidney disease
- Type 2 diabetes mellitus with chronic kidney disease due to conditions classified to .21 and .22
- Use additional code to identify stage of chronic kidney disease (N18.1-N18.6)
- E11.29 Type 2 diabetes mellitus with other diabetic kidney complication
- Type 2 diabetes mellitus with renal tubular degeneration
- E11.21 Type 2 diabetes mellitus with diabetic nephropathy
- E11.3 Type 2 diabetes mellitus with ophthalmic complications
- E11.31 Type 2 diabetes mellitus with unspecified diabetic retinopathy
- E11.311 Type 2 diabetes mellitus with unspecified diabetic retinopathy with macular edema
- E11.319 Type 2 diabetes mellitus with unspecified diabetic retinopathy without macular edema
- E11.32 Type 2 diabetes mellitus with mild nonproliferative diabetic retinopathy
- Type 2 diabetes mellitus with nonproliferative diabetic retinopathy NOS
- E11.321 Type 2 diabetes mellitus with mild nonproliferative diabetic retinopathy with macular edema
- E11.329 Type 2 diabetes mellitus with mild nonproliferative diabetic retinopathy without macular edema
- E11.33 Type 2 diabetes mellitus with moderate nonproliferative diabetic retinopathy
- E11. 331 Type 2 diabetes mellitus with moderate nonproliferative diabetic retinopathy with macular edema
- E11.339 Type 2 diabetes mellitus with moderate nonproliferative diabetic retinopathy without macular edema
- E11.34 Type 2 diabetes mellitus with severe nonproliferative diabetic retinopathy
- E11.341 Type 2 diabetes mellitus with severe nonproliferative diabetic retinopathy with macular edema
- E11.349 Type 2 diabetes mellitus with severe nonproliferative diabetic retinopathy without macular edema
- E11.35 Type 2 diabetes mellitus with proliferative diabetic retinopathy
- E11.351 Type 2 diabetes mellitus with proliferative diabetic retinopathy with macular edema
- E11.359 Type 2 diabetes mellitus with proliferative diabetic retinopathy without macular edema
- E11.36 Type 2 diabetes mellitus with diabetic cataract
- E11.39 Type 2 diabetes mellitus with other diabetic ophthalmic complication
- E11.31 Type 2 diabetes mellitus with unspecified diabetic retinopathy
- E11.4 Type 2 diabetes mellitus with neurological comp``lications
- E11.40 Type 2 diabetes mellitus with diabetic neuropathy, unspecified
- E11.41 Type 2 diabetes mellitus with diabetic mononeuropathy
- E11.42 Type 2 diabetes mellitus with diabetic polyneuropathy
- Type 2 diabetes mellitus with diabetic neuralgia
- E11.43 Type 2 diabetes mellitus with diabetic autonomic (poly)neuropathy
- Type 2 diabetes mellitus with diabetic gastroparesis
- E11.44 Type 2 diabetes mellitus with diabetic amyotrophy
- E11.49 Type 2 diabetes mellitus with other diabetic neurological complication
- E11.5 Type 2 diabetes mellitus with circulatory complications
- E11.51 Type 2 diabetes mellitus with diabetic peripheral angiopathy without gangrene
- E11.52 Type 2 diabetes mellitus with diabetic peripheral angiopathy with gangrene
- Type 2 diabetes mellitus with diabetic gangrene
- E11.59 Type 2 diabetes mellitus with other circulatory complications
- E11.6 Type 2 diabetes mellitus with other specified complications
- E11. 61 Type 2 diabetes mellitus with diabetic arthropathy
- E11.610 Type 2 diabetes mellitus with diabetic neuropathic arthropathy
- Type 2 diabetes mellitus with Charcot's joints
- E11.618 Type 2 diabetes mellitus with other diabetic arthropathy
- E11.610 Type 2 diabetes mellitus with diabetic neuropathic arthropathy
- E11.62 Type 2 diabetes mellitus with skin complications
- E11.620 Type 2 diabetes mellitus with diabetic dermatitis
- Type 2 diabetes mellitus with diabetic necrobiosis lipoidica
- E11.621 Type 2 diabetes mellitus with foot ulcer
- Use additional code to identify site of ulcer (L97.4-, L97.5-)
- E11.622 Type 2 diabetes mellitus with other skin ulcer
- Use additional code to identify site of ulcer (L97.1-L97.9, L98.41-L98.49)
- E11.628 Type 2 diabetes mellitus with other skin complications
- E11.620 Type 2 diabetes mellitus with diabetic dermatitis
- E11.63 Type 2 diabetes mellitus with oral complications
- E11.630 Type 2 diabetes mellitus with periodontal disease
- E11.638 Type 2 diabetes mellitus with other oral complications
- E11.64 Type 2 diabetes mellitus with hypoglycemia
- E11.641 Type 2 diabetes mellitus with hypoglycemia with coma
- E11.649 Type 2 diabetes mellitus with hypoglycemia without coma
- E11.65 Type 2 diabetes mellitus with hyperglycemia
- E11.69 Type 2 diabetes mellitus with other specified complication
- Use additional code to identify complication
- E11. 61 Type 2 diabetes mellitus with diabetic arthropathy
- E11.8 Type 2 diabetes mellitus with unspecified complications
- E11.9 Type 2 diabetes mellitus without complications
E13 Other specified diabetes mellitus
edit- Includes: diabetes mellitus due to genetic defects of beta-cell function
- diabetes mellitus due to genetic defects in insulin action
- Use additional code to identify any insulin use (Z79.4)
- Excludes1: diabetes (mellitus) due to autoimmune process (E10.-)
- diabetes (mellitus) due to immune mediated pancreatic islet beta-cell destruction (E10.-)
- diabetes mellitus due to underlying condition (E08.-)
- drug or chemical induced diabetes mellitus (E09.-)
- gestational diabetes (O24.44)
- neonatal diabetes mellitus (P70.2)
- type 2 diabetes mellitus (E11.-)
- E13.0 Other specified diabetes mellitus with hyperosmolarity
- E13.00 Other specified diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC)
- E13.01 Other specified diabetes mellitus with hyperosmolarity with coma
- E13.1 Other specified diabetes mellitus with ketoacidosis
- E13.10 Other specified diabetes mellitus with ketoacidosis without coma
- E13.11 Other specified diabetes mellitus with ketoacidosis with coma
- E13.2 Other specified diabetes mellitus with kidney complications
- E13.21 Other specified diabetes mellitus with diabetic nephropathy
- Other specified diabetes mellitus with intercapillary glomerulosclerosis
- Other specified diabetes mellitus with intracapillary glomerulonephrosis
- Other specified diabetes mellitus with Kimmelstiel-Wilson disease
- E13.22 Other specified diabetes mellitus with diabetic chronic kidney disease
- Other specified diabetes mellitus with chronic kidney disease due to conditions classified to .21 and .22
- Use additional code to identify stage of chronic kidney disease (N18.1-N18.6)
- E13.29 Other specified diabetes mellitus with other diabetic kidney complication
- Other specified diabetes mellitus with renal tubular degeneration
- E13.21 Other specified diabetes mellitus with diabetic nephropathy
- E13.3 Other specified diabetes mellitus with ophthalmic complications
- E13.31 Other specified diabetes mellitus with unspecified diabetic retinopathy
- E13.311 Other specified diabetes mellitus with unspecified diabetic retinopathy with macular edema
- E13.319 Other specified diabetes mellitus with unspecified diabetic retinopathy without macular edema
- E13. 32 Other specified diabetes mellitus with mild nonproliferative diabetic retinopathy
- Other specified diabetes mellitus with nonproliferative diabetic retinopathy NOS
- E13.321 Other specified diabetes mellitus with mild nonproliferative diabetic retinopathy with macular edema
- E13.329 Other specified diabetes mellitus with mild nonproliferative diabetic retinopathy without macular edema
- E13.33 Other specified diabetes mellitus with moderate nonproliferative diabetic retinopathy
- E13.331 Other specified diabetes mellitus with moderate nonproliferative diabetic retinopathy with macular edema
- E13.339 Other specified diabetes mellitus with moderate nonproliferative diabetic retinopathy without macular edema
- E13.34 Other specified diabetes mellitus with severe nonproliferative diabetic retinopathy
- E13.341 Other specified diabetes mellitus with severe nonproliferative diabetic retinopathy with macular edema
- E13.349 Other specified diabetes mellitus with severe nonproliferative diabetic retinopathy without macular edema
- E13.35 Other specified diabetes mellitus with proliferative diabetic retinopathy
- E13.351 Other specified diabetes mellitus with proliferative diabetic retinopathy with macular edema
- E13.359 Other specified diabetes mellitus with proliferative diabetic retinopathy without macular edema
- E13.36 Other specified diabetes mellitus with diabetic cataract
- E13.39 Other specified diabetes mellitus with other diabetic ophthalmic complication
- E13.31 Other specified diabetes mellitus with unspecified diabetic retinopathy
- E13.4 Other specified diabetes mellitus with neurological complications
- E13.40 Other specified diabetes mellitus with diabetic neuropathy, unspecified
- E13.41 Other specified diabetes mellitus with diabetic mononeuropathy
- E13.42 Other specified diabetes mellitus with diabetic polyneuropathy
- Other specified diabetes mellitus with diabetic neuralgia
- E13. 43 Other specified diabetes mellitus with diabetic autonomic (poly)neuropathy
- Other specified diabetes mellitus with diabetic gastroparesis
- E13.44 Other specified diabetes mellitus with diabetic amyotrophy
- E13.49 Other specified diabetes mellitus with other diabetic neurological complication
- E13.5 Other specified diabetes mellitus with circulatory complications
- E13.51 Other specified diabetes mellitus with diabetic peripheral angiopathy without gangrene
- E13.52 Other specified diabetes mellitus with diabetic peripheral angiopathy with gangrene
- Other specified diabetes mellitus with diabetic gangrene
- E13.59 Other specified diabetes mellitus with other circulatory complications
- E13.6 Other specified diabetes mellitus with other specified complications
- E13.61 Other specified diabetes mellitus with diabetic arthropathy
- E13.610 Other specified diabetes mellitus with diabetic neuropathic arthropathy
- Other specified diabetes mellitus with Charcot's joints
- E13.618 Other specified diabetes mellitus with other diabetic arthropathy
- E13.610 Other specified diabetes mellitus with diabetic neuropathic arthropathy
- E13.62 Other specified diabetes mellitus with skin complications
- E13.620 Other specified diabetes mellitus with diabetic dermatitis
- Other specified diabetes mellitus with diabetic necrobiosis lipoidica
- E13.621 Other specified diabetes mellitus with foot ulcer
- Use additional code to identify site of ulcer (L97.4-, L97.5-)
- E13.622 Other specified diabetes mellitus with other skin ulcer
- Use additional code to identify site of ulcer (L97.1-L97.9, L98.41-L98.49)
- E13.628 Other specified diabetes mellitus with other skin complications
- E13.620 Other specified diabetes mellitus with diabetic dermatitis
- E13.63 Other specified diabetes mellitus with oral complications
- E13.630 Other specified diabetes mellitus with periodontal disease
- E13. 638 Other specified diabetes mellitus with other oral complications
- E13.64 Other specified diabetes mellitus with hypoglycemia
- E13.641 Other specified diabetes mellitus with hypoglycemia with coma
- E13.649 Other specified diabetes mellitus with hypoglycemia without coma
- E13.65 Other specified diabetes mellitus with hyperglycemia
- E13.69 Other specified diabetes mellitus with other specified complication
- Use additional code to identify complication
- E13.61 Other specified diabetes mellitus with diabetic arthropathy
- E13.8 Other specified diabetes mellitus with unspecified complications
- E13.9 Other specified diabetes mellitus without complications
Other disorders of glucose regulation and pancreatic internal secretion (E15-E16)
editE15 Nondiabetic hypoglycemic coma
edit- Includes: drug-induced insulin coma in nondiabetic
- hyperinsulinism with hypoglycemic coma
- hypoglycemic coma NOS
E16 Other disorders of pancreatic internal secretion
edit- E16.0 Drug-induced hypoglycemia without coma
- Code first (T36-T50) to identify drug
- E16.1 Other hypoglycemia
- Functional hyperinsulinism
- Functional nonhyperinsulinemic hypoglycemia
- Hyperinsulinism NOS
- Hyperplasia of pancreatic islet beta cells NOS
- Excludes1: hypoglycemia in infant of diabetic mother (P70.1)
- neonatal hypoglycemia (P70.4)
- E16.2 Hypoglycemia, unspecified
- E16.3 Increased secretion of glucagon
- Hyperplasia of pancreatic endocrine cells with glucagon excess
- E16.4 Increased secretion of gastrin
- Hypergastrinemia
- Hyperplasia of pancreatic endocrine cells with gastrin excess
- Zollinger-Ellison syndrome
- E16.8 Other specified disorders of pancreatic internal secretion
- Increased secretion from endocrine pancreas of growth hormone-releasing hormone
- Increased secretion from endocrine pancreas of pancreatic polypeptide
- Increased secretion from endocrine pancreas of somatostatin
- Increased secretion from endocrine pancreas of vasoactive-intestinal polypeptide
- E16.9 Disorder of pancreatic internal secretion, unspecified
- Islet-cell hyperplasia NOS
- Pancreatic endocrine cell hyperplasia NOS
Disorders of other endocrine glands (E20-E35)
edit- Excludes1: galactorrhea (N64.3)
- gynecomastia (N62)
E20 Hypoparathyroidism
edit- Excludes1: Di George's syndrome (D82.1)
- postprocedural hypoparathyroidism (E89.2)
- tetany NOS (R29.0 )
- transitory neonatal hypoparathyroidism (P71.4)
- E20.0 Idiopathic hypoparathyroidism
- E20.1 Pseudohypoparathyroidism
- E20.8 Other hypoparathyroidism
- E20.9 Hypoparathyroidism, unspecified
- Parathyroid tetany
E21 Hyperparathyroidism and other disorders of parathyroid gland
edit- Excludes1: adult osteomalacia (M83.-)
- ectopic hyperparathyroidism (E34.2)
- familial hypocalciuric hypercalcemia (E83.52)
- hungry bone syndrome (E83.81)
- infantile and juvenile osteomalacia (E55.0)
- E21.0 Primary hyperparathyroidism
- Hyperplasia of parathyroid
- Osteitis fibrosa cystica generalisata [von Recklinghausen's disease of bone]
- E21.1 Secondary hyperparathyroidism, not elsewhere classified
- Excludes1: secondary hyperparathyroidism of renal origin (N25.81)
- E21.2 Other hyperparathyroidism
- Tertiary hyperparathyroidism
- Excludes1: familial hypocalciuric hypercalcemia (E83.52)
- E21.3 Hyperparathyroidism, unspecified
- E21.4 Other specified disorders of parathyroid gland
- E21.5 Disorder of parathyroid gland, unspecified
E22 Hyperfunction of pituitary gland
edit- Excludes1: Cushing's syndrome (E24.-)
- Nelson's syndrome (E24.1)
- overproduction of ACTH not associated with Cushing's disease (E27.0)
- overproduction of pituitary ACTH (E24.0)
- overproduction of thyroid-stimulating hormone (E05.8-)
- E22.0 Acromegaly and pituitary gigantism
- Overproduction of growth hormone
- Excludes1: constitutional gigantism (E34.4)
- constitutional tall stature (E34.4)
- increased secretion from endocrine pancreas of growth hormone-releasing hormone (E16.8)
- E22.1 Hyperprolactinemia
- E22.2 Syndrome of inappropriate secretion of antidiuretic hormone
- E22.8 Other hyperfunction of pituitary gland
- Central precocious puberty
- E22.9 Hyperfunction of pituitary gland, unspecified
E23 Hypofunction and other disorders of the pituitary gland
edit- Includes: the listed conditions whether the disorder is in the pituitary or the hypothalamus
- Excludes1: postprocedural hypopituitarism (E89.3)
- E23.0 Hypopituitarism
- Fertile eunuch syndrome
- Hypogonadotropic hypogonadism
- Idiopathic growth hormone deficiency
- Isolated deficiency of gonadotropin
- Isolated deficiency of growth hormone
- Isolated deficiency of pituitary hormone
- Kallmann's syndrome
- Lorain-Levi short stature
- Necrosis of pituitary gland (postpartum)
- Panhypopituitarism
- Pituitary cachexia
- Pituitary insufficiency NOS
- Pituitary short stature
- Sheehan's syndrome
- Simmonds' disease
- E23.1 Drug-induced hypopituitarism
- Code first (T36-T50) to identify drug
- E23.2 Diabetes insipidus
- Excludes1: nephrogenic diabetes insipidus (N25.1)
- E23.3 Hypothalamic dysfunction, not elsewhere classified
- Excludes1: Prader-Willi syndrome (Q87.1)
- Russell-Silver syndrome (Q87.1)
- Excludes1: Prader-Willi syndrome (Q87.1)
- E23.6 Other disorders of pituitary gland
- Abscess of pituitary
- Adiposogenital dystrophy
- E23.7 Disorder of pituitary gland, unspecified
E24 Cushing's syndrome
edit- Excludes1: congenital adrenal hyperplasia (E25.0)
- E24.0 Pituitary-dependent Cushing's disease
- Overproduction of pituitary ACTH
- Pituitary-dependent hypercorticalism
- E24.1 Nelson's syndrome
- E24.2 Drug-induced Cushing's syndrome
- Code first (T36-T50) to identify drug
- E24.3 Ectopic ACTH syndrome
- E24.4 Alcohol-induced pseudo-Cushing's syndrome
- E24.8 Other Cushing's syndrome
- E24.9 Cushing's syndrome, unspecified
E25 Adrenogenital disorders
edit- Includes: adrenogenital syndromes, virilizing or feminizing, whether acquired or due to adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis
- female:
- adrenal pseudohermaphroditism
- heterosexual precocious pseudopuberty
- male:
- isosexual precocious pseudopuberty
- macrogenitosomia praecox
- sexual precocity with adrenal hyperplasia
- virilization (female)
- Excludes1: indeterminate sex and pseudohermaphroditism (Q56)
- chromosomal abnormalities (Q90-Q99)
- E25.0 Congenital adrenogenital disorders associated with enzyme deficiency
- Congenital adrenal hyperplasia
- 21-Hydroxylase deficiency
- Salt-losing congenital adrenal hyperplasia
- E25.8 Other adrenogenital disorders
- Idiopathic adrenogenital disorder
- E25.9 Adrenogenital disorder, unspecified
- Adrenogenital syndrome NOS
E26 Hyperaldosteronism
edit- E26.0 Primary hyperaldosteronism
- E26.01 Conn's syndrome
- Code also adrenal adenoma (D35.0)
- E26.02 Glucocorticoid-remediable aldosteronism
- Familial aldosteronism type I
- E26.09 Other primary hyperaldosteronism
- Primary aldosteronism due to adrenal hyperplasia (bilateral)
- E26.01 Conn's syndrome
- E26.1 Secondary hyperaldosteronism
- E26.8 Other hyperaldosteronism
- E26. 81 Bartter?s syndrome
- E26.89 Other hyperaldosteronism
- E26.9 Hyperaldosteronism, unspecified
- Aldosteronism NOS
- Hyperaldosteronism NOS
E27 Other disorders of adrenal gland
edit- E27.0 Other adrenocortical overactivity
- Overproduction of ACTH, not associated with Cushing's disease
- Premature adrenarche
- Excludes1: Cushing's syndrome (E24.-)
- E27.1 Primary adrenocortical insufficiency
- Addison's disease
- Autoimmune adrenalitis
- Excludes1: Addison only phenotype adrenoleukodystrophy (E71.428)
- amyloidosis (E85.-)
- tuberculous Addison's disease (A18.7)
- Waterhouse-Friderichsen syndrome (A39.1)
- E27.2 Addisonian crisis
- Adrenal crisis
- Adrenocortical crisis
- E27.3 Drug-induced adrenocortical insufficiency
- Code first (T36-T50) to identify drug
- E27.4 Other and unspecified adrenocortical insufficiency
- Excludes1: adrenoleukodystrophy [Addison-Schilder] (E71.3-)
- Waterhouse-Friderichsen syndrome (A39.1)
- E27.40 Unspecified adrenocortical insufficiency
- Adrenocortical insufficiency NOS
- Hypoaldosteronism
- E27.49 Other adrenocortical insufficiency
- Adrenal hemorrhage
- Adrenal infarction
- Excludes1: adrenoleukodystrophy [Addison-Schilder] (E71.3-)
- E27.5 Adrenomedullary hyperfunction
- Adrenomedullary hyperplasia
- Catecholamine hypersecretion
- E27.8 Other specified disorders of adrenal gland
- Abnormality of cortisol-binding globulin
- E27.9 Disorder of adrenal gland, unspecified
E28 Ovarian dysfunction
edit- Excludes1: isolated gonadotropin deficiency (E23.0)
- postprocedural ovarian failure (E89.4-)
- E28.0 Estrogen excess
- E28.1 Androgen excess
- Hypersecretion of ovarian androgens
- E28.2 Polycystic ovarian syndrome
- Sclerocystic ovary syndrome
- SteinLeventhal syndrome
- E28.3 Primary ovarian failure
- Excludes1: pure gonadal dysgenesis (Q99.1)
- Turner's syndrome (Q96.-)
- E28.31 Premature menopause
- E28.310 Symptomatic premature menopause
- Symptoms such as flushing, sleeplessness, headache, lack of concentration, associated with premature menopause
- E28.319 Asymptomatic premature menopause
- Premature menopause NOS
- E28.310 Symptomatic premature menopause
- E28.39 Other primary ovarian failure
- Decreased estrogen
- Resistant ovary syndrome
- Excludes1: pure gonadal dysgenesis (Q99.1)
- E28.8 Other ovarian dysfunction
- Ovarian hyperfunction NOS
- Excludes1: postprocedural ovarian failure (E89.4-)
- E28.9 Ovarian dysfunction, unspecified
E29 Testicular dysfunction
edit- Excludes1: androgen insensitivity syndrome (E34.5-)
- azoospermia or oligospermia NOS (N46.0-N46.1)
- isolated gonadotropin deficiency (E23.0)
- Klinefelter's syndrome (Q98.0-Q98.2, Q98.4)
- E29.0 Testicular hyperfunction
- Hypersecretion of testicular hormones
- E29.1 Testicular hypofunction
- Defective biosynthesis of testicular androgen NOS
- 5-delta-Reductase deficiency (with male pseudohermaphroditism)
- Testicular hypogonadism NOS
- Excludes1: postprocedural testicular hypofunction (E89.5)
- E29.8 Other testicular dysfunction
- E29.9 Testicular dysfunction, unspecified
E30 Disorders of puberty, not elsewhere classified
edit- E30.0 Delayed puberty
- Constitutional delay of puberty
- Delayed sexual development
- E30.1 Precocious puberty
- Precocious menstruation
- Excludes1: Albright (-McCune) (-Sternberg) syndrome (Q78.1)
- central precocious puberty (E22.8)
- congenital adrenal hyperplasia (E25.0)
- female heterosexual precocious pseudopuberty (E25.-)
- male isosexual precocious pseudopuberty (E25.-)
- E30.8 Other disorders of puberty
- Premature thelarche
- E30. 9 Disorder of puberty, unspecified
E31 Polyglandular dysfunction
edit- Excludes1: ataxia telangiectasia [Louis-Bar] (G11.3)
- dystrophia myotonica [Steinert] (G71.11)
- pseudohypoparathyroidism (E20.1)
- E31.0 Autoimmune polyglandular failure
- Schmidt's syndrome
- E31.1 Polyglandular hyperfunction
- Excludes1: multiple endocrine adenomatosis (E31.2-)
- multiple endocrine neoplasia (E31.2-)
- Excludes1: multiple endocrine adenomatosis (E31.2-)
- E31.2 Multiple endocrine neoplasia [MEN] syndromes
- Multiple endocrine adenomatosis
- Code also any associated malignancies and other conditions associated with the syndromes
- E31.20 Multiple endocrine neoplasia [MEN] syndrome, unspecified
- Multiple endocrine adenomatosis NOS
- Multiple endocrine neoplasia [MEN] syndrome NOS
- E31.21 Multiple endocrine neoplasia [MEN] type I
- Wermer's syndrome
- E31.22 Multiple endocrine neoplasia [MEN] type IIA
- Sipple's syndrome
- E31.23 Multiple endocrine neoplasia [MEN] type IIB
- E31.8 Other polyglandular dysfunction
- E31.9 Polyglandular dysfunction, unspecified
E32 Diseases of thymus
edit- Excludes1: aplasia or hypoplasia of thymus with immunodeficiency (D82.1)
- myasthenia gravis (G70.0)
- E32.0 Persistent hyperplasia of thymus
- Hypertrophy of thymus
- E32.1 Abscess of thymus
- E32.8 Other diseases of thymus
- Excludes1: aplasia or hypoplasia with immunodeficiency (D82.1)
- thymoma (D15.0)
- Excludes1: aplasia or hypoplasia with immunodeficiency (D82.1)
- E32.9 Disease of thymus, unspecified
E34 Other endocrine disorders
edit- Excludes1: pseudohypoparathyroidism (E20.1)
- E34.0 Carcinoid syndrome
- Note: May be used as an additional code to identify functional activity associated with a carcinoid tumor.
- E34.1 Other hypersecretion of intestinal hormones
- E34.2 Ectopic hormone secretion, not elsewhere classified
- Excludes1: ectopic ACTH syndrome (E24.3)
- E34.3 Short stature due to endocrine disorder
- Constitutional short stature
- Larontype short stature
- Excludes1: achondroplastic short stature (Q77.4)
- hypochondroplastic short stature (Q77.4)
- nutritional short stature (E45)
- pituitary short stature (E23.0)
- progeria (E34.8)
- renal short stature (N25.0)
- Russell-Silver syndrome (Q87.1)
- short-limbed stature with immunodeficiency (D82.2)
- short stature in specific dysmorphic syndromes - code to syndrome - see Alphabetical Index
- short stature NOS (R62.52)
- E34.4 Constitutional tall stature
- Constitutional gigantism
- E34.5 Androgen insensitivity syndrome
- E34.50 Androgen insensitivity syndrome, unspecified
- Androgen insensitivity NOS
- E34.51 Complete androgen insensitivity syndrome
- Complete androgen insensitivity
- de Quervain syndrome
- Goldberg-Maxwell syndrome
- E34.52 Partial androgen insensitivity syndrome
- Partial androgen insensitivity
- Reifenstein syndrome
- E34.50 Androgen insensitivity syndrome, unspecified
- E34.8 Other specified endocrine disorders
- Pineal gland dysfunction
- Progeria
- Excludes2: pseudohypoparathyroidism (E20.1)
- E34.9 Endocrine disorder, unspecified
- Endocrine disturbance NOS
- Hormone disturbance NOS
E35 Disorders of endocrine glands in diseases classified elsewhere
edit- Code first underlying disease, such as:
- late congenital syphilis of thymus gland [Dubois disease] (A50.5)
- tuberculous calcification of adrenal gland (B90.8)
- Excludes1: Echinococcus granulosus infection of thyroid gland (B67.3)
- meningococcal hemorrhagic adrenalitis (A39.1)
- syphilis of endocrine gland (A52.79)
- tuberculosis of:
- adrenal gland, except calcification (A18.7)
- endocrine gland NEC (A18.82)
- thyroid gland (A18.81)
- Waterhouse-Friderichsen syndrome (A39.1)
E36 Intraoperative complications of endocrine system
edit- Excludes2: postprocedural endocrine and metabolic complications and disorders, not elsewhere classified (E89.-)
- E36.0 Intraoperative hemorrhage and hematoma of an endocrine system organ or structure complicating a procedure
- Excludes1: intraoperative hemorrhage and hematoma of an endocrine system organ or structure due to accidental puncture or laceration during a procedure (E36.1-)
- E36.01 Intraoperative hemorrhage and hematoma of an endocrine system organ or structure complicating an endocrine system procedure
- E36.02 Intraoperative hemorrhage and hematoma of an endocrine system organ or structure complicating other procedure
- E36.1 Accidental puncture and laceration of an endocrine system organ or structure during a procedure
- E36.11 Accidental puncture and laceration of an endocrine system organ or structure during an endocrine system procedure
- E36.12 Accidental puncture and laceration of an endocrine system organ or structure during other procedure
- E36.8 Other intraoperative complications of endocrine system
- Use additional code, if applicable, to further specify disorder
Malnutrition (E40-E46)
edit- Excludes1: intestinal malabsorption (K90.-)
- sequelae of protein-calorie malnutrition (E64.0)
- Excludes2: nutritional anemias (D50-D53)
- starvation (T73.0)
E40 Kwashiorkor
edit- Includes: severe malnutrition with nutritional edema with dyspigmentation of skin and hair
- Excludes1: marasmic kwashiorkor (E42)
E41 Nutritional marasmus
edit- Includes: severe malnutrition with marasmus
- Excludes1: marasmic kwashiorkor (E42)
E42 Marasmic kwashiorkor
edit- Includes: severe protein-calorie malnutrition with signs of both kwashiorkor and marasmus
- intermediate form severe protein-calorie malnutrition
E43 Unspecified severe protein-calorie malnutrition
edit- Includes: starvation edema
E44 Protein-calorie malnutrition of moderate and mild degree
- E44.0 Moderate protein-calorie malnutrition
- E44.1 Mild protein-calorie malnutrition
E45 Retarded development following protein-calorie malnutrition
edit- Includes: nutritional short stature
- nutritional stunting
- physical retardation due to malnutrition
E46 Unspecified protein-calorie malnutrition
edit- Includes: malnutrition NOS
- protein-calorie imbalance NOS
- Excludes1: nutritional deficiency NOS (E63.9)
Other nutritional deficiencies (E50-E64)
edit- Excludes2: nutritional anemias (D50-D53)
E50 Vitamin A deficiency
edit- Excludes1: sequelae of vitamin A deficiency (E64.1)
- E50.0 Vitamin A deficiency with conjunctival xerosis
- E50.1 Vitamin A deficiency with Bitot's spot and conjunctival xerosis
- Bitot's spot in the young child
- E50.2 Vitamin A deficiency with corneal xerosis
- E50.3 Vitamin A deficiency with corneal ulceration and xerosis
- E50.4 Vitamin A deficiency with keratomalacia
- E50.5 Vitamin A deficiency with night blindness
- E50.6 Vitamin A deficiency with xerophthalmic scars of cornea
- E50.7 Other ocular manifestations of vitamin A deficiency
- Xerophthalmia NOS
- E50.8 Other manifestations of vitamin A deficiency
- Follicular keratosis
- Xeroderma
- E50.9 Vitamin A deficiency, unspecified
- Hypovitaminosis A NOS
E51 Thiamine deficiency
edit- Excludes1: sequelae of thiamine deficiency (E64.8)
- E51.1 Beriberi
- E51.11 Dry beriberi
- Beriberi NOS
- Beriberi with polyneuropathy
- E51.12 Wet beriberi
- Beriberi with cardiovascular manifestations
- Cardiovascular beriberi
- Shoshin disease
- E51.11 Dry beriberi
- E51. 2 Wernicke's encephalopathy
- E51.8 Other manifestations of thiamine deficiency
- E51.9 Thiamine deficiency, unspecified
E52 Niacin deficiency [pellagra]
edit- Includes: niacin (-tryptophan) deficiency
- nicotinamide deficiency
- pellagra (alcoholic)
- Excludes1: sequelae of niacin deficiency (E64.8)
E53 Deficiency of other B group vitamins
edit- Excludes1: sequelae of vitamin B deficiency (E64.8)
- E53.0 Riboflavin deficiency
- Ariboflavinosis
- Vitamin B2 deficiency
- E53.1 Pyridoxine deficiency
- Vitamin B6 deficiency
- Excludes1: pyridoxine-responsive sideroblastic anemia (D64.3)
- E53.8 Deficiency of other specified B group vitamins
- Biotin deficiency
- Cyanocobalamin deficiency
- Folate deficiency
- Folic acid deficiency
- Pantothenic acid deficiency
- Vitamin B12 deficiency
- Excludes1: folate deficiency anemia (D52.-)
- vitamin B12 deficiency anemia (D51.-)
- E53.9 Vitamin B deficiency, unspecified
E54 Ascorbic acid deficiency
edit- Includes: deficiency of vitamin C
- scurvy
- Excludes1: scorbutic anemia (D53.2)
- sequelae of vitamin C deficiency (E64.2)
E55 Vitamin D deficiency
edit- Excludes1: adult osteomalacia (M83.-)
- osteoporosis (M80-)
- sequelae of rickets (E64.3)
- E55.0 Rickets, active
- Infantile Osteomalacia
- Juvenile Osteomalacia
- Excludes1: celiac rickets (K90.0)
- Crohn's rickets (K50.-)
- hereditary vitamin D-dependent rickets (E83.32)
- inactive rickets (E64.3)
- renal rickets (N25.0)
- sequelae of rickets (E64.3)
- vitamin D-resistant rickets (E83.31)
- E55.9 Vitamin D deficiency, unspecified
- Avitaminosis D
E56 Other vitamin deficiencies
edit- Excludes1: sequelae of other vitamin deficiencies (E64.8)
- E56.0 Deficiency of vitamin E
- E56.1 Deficiency of vitamin K
- Excludes1: deficiency of coagulation factor due to vitamin K deficiency (D68.4)
- vitamin K deficiency of newborn (P53)
- Excludes1: deficiency of coagulation factor due to vitamin K deficiency (D68.4)
- E56.8 Deficiency of other vitamins
- E56.9 Vitamin deficiency, unspecified
E58 Dietary calcium deficiency
edit- Excludes1: disorders of calcium metabolism (E83.5)
- sequelae of calcium deficiency (E64.8)
E59 Dietary selenium deficiency
edit- Includes: Keshan disease
- Excludes1: sequelae of selenium deficiency (E64.8)
E60 Dietary zinc deficiency
editE61 Deficiency of other nutrient elements
edit- Excludes1: disorders of mineral metabolism (E83.-)
- iodine deficiency related thyroid disorders (E00-E02)
- sequelae of malnutrition and other nutritional deficiencies (E64.-)
- E61.0 Copper deficiency
- E61.1 Iron deficiency
- Excludes1: iron deficiency anemia (D50.-)
- E61.2 Magnesium deficiency
- E61.3 Manganese deficiency
- E61.4 Chromium deficiency
- E61.5 Molybdenum deficiency
- E61.6 Vanadium deficiency
- E61.7 Deficiency of multiple nutrient elements
- E61.8 Deficiency of other specified nutrient elements
- E61.9 Deficiency of nutrient element, unspecified
E63 Other nutritional deficiencies
edit- Excludes1: dehydration (E86.0)
- failure to thrive, adult (R62.7)
- failure to thrive, child (R62.51)
- feeding problems in newborn (P92.-)
- sequelae of malnutrition and other nutritional deficiencies (E64.-)
- E63.0 Essential fatty acid [EFA] deficiency
- E63.1 Imbalance of constituents of food intake
- E63.8 Other specified nutritional deficiencies
- E63.9 Nutritional deficiency, unspecified
E64 Sequelae of malnutrition and other nutritional deficiencies
edit- This category is to be used to indicate conditions in categories E43, E44, E46, E50-E63 as the cause of sequelae, which are themselves classified elsewhere. The "sequelae" include conditions specified as such; they also include the late effects of diseases classifiable to the above categories if the disease itself is no longer present
- Code first condition resulting from (sequela) of malnutrition and other nutritional deficiencies
- E64.0 Sequelae of protein-calorie malnutrition
- Excludes2: retarded development following protein-calorie malnutrition (E45)
- E64.1 Sequelae of vitamin A deficiency
- E64.2 Sequelae of vitamin C deficiency
- E64.3 Sequelae of rickets
- E64.8 Sequelae of other nutritional deficiencies
- E64.9 Sequelae of unspecified nutritional deficiency
Overweight, obesity and other hyperalimentation (E65-E68)
editE65 Localized adiposity
edit- Fat pad
E66 Overweight and obesity
edit- Code first: obesity complicating pregnancy, childbirth and the puerperium, if applicable (O99.21-)
- Use additional code to identify body mass index (BMI), if known (Z68.-)
- Excludes1: adiposogenital dystrophy (E23.6)
- lipomatosis NOS (E88.2)
- lipomatosis dolorosa [Dercum] (E88.2)
- Prader-Willi syndrome (Q87.1)
- E66.0 Obesity due to excess calories
- E66.01 Morbid (severe) obesity due to excess calories
- Excludes1: morbid (severe) obesity with alveolar hypoventilation (E66.2)
- E66.09 Other obesity due to excess calories
- E66.01 Morbid (severe) obesity due to excess calories
- E66.1 Drug-induced obesity
- Code first (T36-T50) to identify drug
- E66. 2 Morbid (severe) obesity with alveolar hypoventilation
- Pickwickian syndrome
- E66.3 Overweight
- E66.8 Other obesity
- E66.9 Obesity, unspecified
- Obesity NOS
E67 Other hyperalimentation
edit- Excludes1: hyperalimentation NOS (R63.2)
- sequelae of hyperalimentation (E68)
- E67.0 Hypervitaminosis A
- E67.1 Hypercarotinemia
- E67.2 Megavitamin-B6 syndrome
- E67.3 Hypervitaminosis D
- E67.8 Other specified hyperalimentation
E68 Sequelae of hyperalimentation
edit- Code first condition resulting from (sequela) of hyperalimentation
Metabolic disorders (E70-E90)
edit- Excludes1: androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- Ehlers-Danlos syndrome (Q79.6)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
E70 Disorders of aromatic amino-acid metabolism
edit- E70.0 Classical phenylketonuria
- E70.1 Other hyperphenylalaninemias
- E70.2 Disorders of tyrosine metabolism
- Excludes1: transitory tyrosinemia of newborn (P74.5)
- E70.20 Disorder of tyrosine metabolism, unspecified
- E70.21 Tyrosinemia
- Hypertyrosinemia
- E70.29 Other disorders of tyrosine metabolism
- Alkaptonuria
- Ochronosis
- E70.3 Albinism
- E70.30 Albinism, unspecified
- E70.31 Ocular albinism
- E70.310 X-linked ocular albinism
- E70.311 Autosomal recessive ocular albinism
- E70.318 Other ocular albinism
- E70.319 Ocular albinism, unspecified
- E70. 32 Oculocutaneous albinism
- Excludes1: Chediak-Higashi syndrome (E70.330)
- Hermansky-Pudlak syndrome (E70.331)
- E70.320 Tyrosinase negative oculocutaneous albinism
- Albinism I
- Oculocutaneous albinism ty-neg
- E70.321 Tyrosinase positive oculocutaneous albinism
- Albinism II
- Oculocutaneous albinism ty-pos
- E70.328 Other oculocutaneous albinism
- Cross syndrome
- E70.329 Oculocutaneous albinism, unspecified
- Excludes1: Chediak-Higashi syndrome (E70.330)
- E70.33 Albinism with hematologic abnormality
- E70.330 Chediak-Higashi syndrome
- E70.331 Hermansky-Pudlak syndrome
- E70.338 Other albinism with hematologic abnormality
- E70.339 Albinism with hematologic abnormality, unspecified
- E70.39 Other specified albinism
- Piebaldism
- E70.4 Disorders of histidine metabolism
- E70.40 Disorders of histidine metabolism, unspecified
- E70.41 Histidinemia
- E70.49 Other disorders of histidine metabolism
- E70.5 Disorders of tryptophan metabolism
- E70.8 Other disorders of aromatic amino-acid metabolism
- E70.9 Disorder of aromatic amino-acid metabolism, unspecified
E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
edit- E71.0 Maple-syrup-urine disease
- E71.1 Other disorders of branched-chain amino-acid metabolism
- E71.11 Branched-chain organic acidurias
- E71.110 Isovaleric acidemia
- E71.111 3-methylglutaconic aciduria
- E71.118 Other branched-chain organic acidurias
- E71.12 Disorders of propionate metabolism
- E71.120 Methylmalonic acidemia
- E71.121 Propionic acidemia
- E71.128 Other disorders of propionate metabolism
- E71.19 Other disorders of branched-chain amino-acid metabolism
- Hyperleucine-isoleucinemia
- Hypervalinemia
- E71.11 Branched-chain organic acidurias
- E71.2 Disorder of branched-chain amino-acid metabolism, unspecified
- E71.3 Disorders of fatty-acid metabolism
- Excludes1: peroxisomal disorders (E71.5)
- Refsum's disease (G60.1)
- Schilder's disease (G37.0)
- Excludes2: carnitine deficiency due to inborn error of metabolism (E71.42)
- E71.30 Disorder of fatty-acid metabolism, unspecified
- E71.31 Disorders of fatty-acid oxidation
- E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
- LCAD
- VLCAD
- E71.311 Medium chain acyl CoA dehydrogenase deficiency
- MCAD
- E71.312 Short chain acyl CoA dehydrogenase deficiency
- SCAD
- E71.313 Glutaric aciduria type II
- Glutaric aciduria type II A
- Glutaric aciduria type II B
- Glutaric aciduria type II C
- Excludes1: glutaric aciduria (type 1) NOS (E72.3)
- E71.314 Muscle carnitine palmitoyltransferase deficiency
- E71.318 Other disorders of fatty-acid oxidation
- E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
- E71.32 Disorders of ketone metabolism
- E71.39 Other disorders of fatty-acid metabolism
- Excludes1: peroxisomal disorders (E71.5)
- E71.4 Disorders of carnitine metabolism
- Excludes1: Muscle carnitine palmitoyltransferase deficiency (E71.314)
- E71.40 Disorder of carnitine metabolism, unspecified
- E71.41 Primary carnitine deficiency
- E71.42 Carnitine deficiency due to inborn errors of metabolism
- Code also associated inborn error or metabolism
- E71.43 Iatrogenic carnitine deficiency
- Carnitine deficiency due to:
- hemodialysis
- Valproic acid therapy
- E71.44 Other secondary carnitine deficiency
- E71.440 Ruvalcaba-Myhre-Smith syndrome
- E71.448 Other secondary carnitine deficiency
- E71.5 Peroxisomal disorders
- Excludes1: Schilder?s disease (G37.0)
- E71.50 Peroxisomal disorder, unspecified
- E71. 51 Disorders of peroxisome biogenesis
- Group 1 peroxisomal disorders
- Excludes1: Refsum's disease (G60.1)
- E71.510 Zellweger syndrome
- E71.511 Neonatal adrenoleukodystrophy
- Excludes1: X-linked adrenoleukodystrophy (E71.42-)
- E71.518 Other disorders of peroxisome biogenesis
- E71.52 X-linked adrenoleukodystrophy
- E71.520 Childhood cerebral X-linked adrenoleukodystrophy
- E71.521 Adolescent X-linked adrenoleukodystrophy
- E71.522 Adrenomyeloneuropathy
- E71.528 Other X-linked adrenoleukodystrophy
- Addison only phenotype adrenoleukodystrophy
- Addison-Schilder adrenoleukodystrophy
- E71.529 X-linked adrenoleukodystrophy, unspecified
- E71.53 Other group 2 peroxisomal disorders
- E71.54 Other peroxisomal disorders
- E71.540 Rhizomelic chondrodysplasia punctata
- Excludes1: chondrodysplasia punctata NOS (Q77.3)
- E71.541 Zellweger-like syndrome
- E71.542 Other group 3 peroxisomal disorders
- E71.548 Other peroxisomal disorders
- E71.540 Rhizomelic chondrodysplasia punctata
E72 Other disorders of amino-acid metabolism
edit- Excludes1: disorders of:
- aromatic amino-acid metabolism (E70.-)
- branched-chain amino-acid metabolism (E71.0-E71.2)
- fatty-acid metabolism (E71.3)
- purine and pyrimidine metabolism (E79.-)
- gout ( M1a-, M10.-)
- E72.0 Disorders of amino-acid transport
- Excludes1: disorders of tryptophan metabolism (E70.5)
- E72.00 Disorders of amino-acid transport, unspecified
- E72.01 Cystinuria
- E72.02 Hartnup's disease
- E72.03 Lowe's syndrome
- Use additional code for associated glaucoma (H42)
- E72.04 Cystinosis
- Fanconi (-de Toni) (-Debr?) syndrome with cystinosis
- Excludes1: Fanconi (-de Toni) (-Debr?) syndrome without cystinosis (E72.09)
- E72.09 Other disorders of amino-acid transport
- Fanconi (-de Toni) (-Debr?) syndrome, unspecified
- E72. 1 Disorders of sulfur-bearing amino-acid metabolism
- Excludes1: cystinosis (E72.04)
- cystinuria (E72.01)
- transcobalamin II deficiency (D51.2)
- E72.10 Disorders of sulfur-bearing amino-acid metabolism, unspecified
- E72.11 Homocystinuria
- Cystathionine synthase deficiency
- E72.12 Methylenetetrahydrofolate reductase deficiency
- E72.19 Other disorders of sulfur-bearing amino-acid metabolism
- Cystathioninuria
- Methioninemia
- Sulfite oxidase deficiency
- Excludes1: cystinosis (E72.04)
- E72.2 Disorders of urea cycle metabolism
- Excludes1: disorders of ornithine metabolism (E72.4)
- E72.20 Disorder of urea cycle metabolism, unspecified
- Hyperammonemia
- Excludes1: hyperammonemia-hyperornithinemia-homocitrullinemia syndrome E72.4
- transient hyperammonemia of newborn (P74.6)
- E72.21 Argininemia
- E72.22 Arginosuccinic aciduria
- E72.23 Citrullinemia
- E72.29 Other disorders of urea cycle metabolism
- E72.3 Disorders of lysine and hydroxylysine metabolism
- Glutaric aciduria NOS
- Glutaric aciduria (type I)
- Hydroxylysinemia
- Hyperlysinemia
- Excludes1: glutaric aciduria type II (E71.313)
- Refsum's disease (G60.1)
- Zellweger syndrome (E71.510)
- E72.4 Disorders of ornithine metabolism
- Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome
- Ornithinemia (types I, II)
- Ornithine transcarbamylase deficiency
- Excludes1: hereditary choroidal dystrophy (H31.2-)
- E72.5 Disorders of glycine metabolism
- E72.50 Disorder of glycine metabolism, unspecified
- E72.51 Non-ketotic hyperglycinemia
- E72.52 Trimethylaminuria
- E72.53 Hyperoxaluria
- Oxalosis
- Oxaluria
- E72. 59 Other disorders of glycine metabolism
- D-glycericacidemia
- Hyperhydroxyprolinemia
- Hyperprolinemia (types I, II)
- Sarcosinemia
- E72.8 Other specified disorders of amino-acid metabolism
- Disorders of beta-amino-acid metabolism
- Disorders of gamma-glutamyl cycle
- E72.9 Disorder of amino-acid metabolism, unspecified
E73 Lactose intolerance
edit- E73.0 Congenital lactase deficiency
- E73.1 Secondary lactase deficiency
- E73.8 Other lactose intolerance
- E73.9 Lactose intolerance, unspecified
E74 Other disorders of carbohydrate metabolism
edit- Excludes1: diabetes mellitus (E09-E13)
- hypoglycemia NOS (E16.2)
- increased secretion of glucagon (E16.3)
- mucopolysaccharidosis (E76.0--E76.3)
- E74.0 Glycogen storage disease
- E74.00 Glycogen storage disease, unspecified
- E74.01 von Gierke disease
- Type I glycogen storage disease
- E74.02 Pompe disease
- Cardiac glycogenosis
- Type II glycogen storage disease
- E74.03 Cori disease
- Forbes disease
- Type III glycogen storage disease
- E74.04 McArdle disease
- Type V glycogen storage disease
- E74.09 Other glycogen storage disease
- Andersen disease
- Hers disease
- Tauri disease
- Glycogen storage disease, types 0, IV, VI-XI
- Liver phosphorylase deficiency
- Muscle phosphofructokinase deficiency
- E74.1 Disorders of fructose metabolism
- Excludes1: muscle phosphofructokinase deficiency (E74.09)
- E74.10 Disorder of fructose metabolism, unspecified
- E74.11 Essential fructosuria
- Fructokinase deficiency
- E74.12 Hereditary fructose intolerance
- Fructosemia
- E74. 19 Other disorders of fructose metabolism
- Fructose-1, 6-diphosphatase deficiency
- E74.2 Disorders of galactose metabolism
- E74.20 Disorders of galactose metabolism, unspecified
- E74.21 Galactosemia
- E74.29 Other disorders of galactose metabolism
- Galactokinase deficiency
- E74.3 Other disorders of intestinal carbohydrate absorption
- Excludes2: lactose intolerance (E73.-)
- E74.31 Sucrase-isomaltase deficiency
- E74.39 Other disorders of intestinal carbohydrate absorption
- Disorder of intestinal carbohydrate absorption NOS
- Glucose-galactose malabsorption
- Sucrase deficiency
- E74.4 Disorders of pyruvate metabolism and gluconeogenesis
- Deficiency of phosphoenolpyruvate carboxykinase
- Deficiency of pyruvate carboxylase
- Deficiency of pyruvate dehydrogenase
- Excludes1: disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
- Leigh?s syndrome (G31.82)
- E74.8 Other specified disorders of carbohydrate metabolism
- Essential pentosuria
- Renal glycosuria
- E74.9 Disorder of carbohydrate metabolism, unspecified
E75 Disorders of sphingolipid metabolism and other lipid storage disorders
edit- Excludes1: mucolipidosis, types I-III (E77.0-E77.1)
- Refsum's disease (G60.1)
- E75.0 GM2 gangliosidosis
- E75.00 GM2 gangliosidosis, unspecified
- E75.01 Sandhoff disease
- E75.02 Tay-Sachs disease
- E75.09 Other GM2 gangliosidosis
- Adult GM2 gangliosidosis
- Juvenile GM2 gangliosidosis
- E75.1 Other and unspecified gangliosidosis
- E75.10 Unspecified gangliosidosis
- Gangliosidosis NOS
- E75.11 Mucolipidosis IV
- E75.19 Other gangliosidosis
- GM1 gangliosidosis
- GM3 gangliosidosis
- E75.10 Unspecified gangliosidosis
- E75.2 Other sphingolipidosis
- Excludes1: adrenoleukodystrophy [Addison-Schilder] (E71.30)
- E75.21 Fabry (-Anderson) disease
- E75.22 Gaucher disease
- E75.23 Krabbe disease
- E75.24 Niemann-Pick disease
- E75.240 Niemann-Pick disease type A
- E75.241 Niemann-Pick disease type B
- E75.242 Niemann-Pick disease type C
- E75.243 Niemann-Pick disease type D
- E75.248 Other Niemann-Pick disease
- E75.249 Niemann-Pick disease, unspecified
- E75.25 Metachromatic leukodystrophy
- E75.29 Other sphingolipidosis
- Farber's syndrome
- Sulfatase deficiency
- Sulfatide lipidosis
- E75.3 Sphingolipidosis, unspecified
- E75.4 Neuronal ceroid lipofuscinosis
- Batten disease
- Bielschowsky-Jansky disease
- Kufs disease
- Spielmeyer-Vogt disease
- E75.5 Other lipid storage disorders
- Cerebrotendinous cholesterosis [van Bogaert-Scherer-Epstein]
- Wolman's disease
- E75.6 Lipid storage disorder, unspecified
E76 Disorders of glycosaminoglycan metabolism
edit- E76.0 Mucopolysaccharidosis, type I
- E76.01 Hurler?s syndrome
- E76.02 Hurler-Scheie syndrome
- E76.03 Scheie?s syndrome
- E76.1 Mucopolysaccharidosis, type II
- Hunter's syndrome
- E76.2 Other mucopolysaccharidoses
- E76.21 Morquio mucopolysaccharidoses
- E76.210 Morquio A mucopolysaccharidoses
- Classic Morquio syndrome
- Morquio syndrome A
- Mucopolysaccharidosis, type IVA
- E76.211 Morquio B mucopolysaccharidoses
- Morquio-like mucopolysaccharidoses
- Morquio-like syndrome
- Morquio syndrome B
- Mucopolysaccharidosis, type IVB
- E76.219 Morquio mucopolysaccharidoses, unspecified
- Morquio syndrome
- Mucopolysaccharidosis, type IV
- E76.210 Morquio A mucopolysaccharidoses
- E76.22 Sanfilippo mucopolysaccharidoses
- Mucopolysaccharidosis, type III (A) (B) (C) (D)
- Sanfilippo A syndrome
- Sanfilippo B syndrome
- Sanfilippo C syndrome
- Sanfilippo D syndrome
- E76.29 Other mucopolysaccharidoses
- beta-Glucuronidase deficiency
- Maroteaux-Lamy (mild) (severe) syndrome
- Mucopolysaccharidosis, types VI, VII
- E76.21 Morquio mucopolysaccharidoses
- E76.3 Mucopolysaccharidosis, unspecified
- E76.8 Other disorders of glucosaminoglycan metabolism
- E76.9 Glucosaminoglycan metabolism disorder, unspecified
E77 Disorders of glycoprotein metabolism
edit- E77.0 Defects in post-translational modification of lysosomal enzymes
- Mucolipidosis II [I-cell disease]
- Mucolipidosis III [pseudo-Hurler polydystrophy]
- E77.1 Defects in glycoprotein degradation
- Aspartylglucosaminuria
- Fucosidosis
- Mannosidosis
- Sialidosis [mucolipidosis I]
- E77.8 Other disorders of glycoprotein metabolism
- E77.9 Disorder of glycoprotein metabolism, unspecified
- E78 Disorders of lipoprotein metabolism and other lipidemias
- Excludes1: sphingolipidosis (E75.0-E75.3)
E78.0 Pure hypercholesterolemia
edit- Familial hypercholesterolemia
- Fredrickson's hyperlipoproteinemia, type IIa
- Hyperbetalipoproteinemia
- Hyperlipidemia, Group A
- Low-density-lipoprotein-type [LDL] hyperlipoproteinemia
- E78.1 Pure hyperglyceridemia
- Elevated fasting triglycerides
- Endogenous hyperglyceridemia
- Fredrickson's hyperlipoproteinemia, type IV
- Hyperlipidemia, group B
- Hyperprebetalipoproteinemia
- Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia
- E78. 2 Mixed hyperlipidemia
- Broad- or floating-betalipoproteinemia
- Combined hyperlipidemia NOS
- Elevated cholesterol with elevated triglycerides NEC
- Fredrickson's hyperlipoproteinemia, type IIb or III
- Hyperbetalipoproteinemia with prebetalipoproteinemia
- Hypercholesteremia with endogenous hyperglyceridemia
- Hyperlipidemia, group C
- Tubo-eruptive xanthoma
- Xanthoma tuberosum
- Excludes1: cerebrotendinous cholesterosis [van Bogaert-Scherer- Epstein] (E75.5)
- familial combined hyperlipidemia (E78.4)
- E78.3 Hyperchylomicronemia
- Chylomicron retention disease
- Fredrickson's hyperlipoproteinemia, type I or V
- Hyperlipidemia, group D
- Mixed hyperglyceridemia
- E78.4 Other hyperlipidemia
- Familial combined hyperlipidemia
- E78.5 Hyperlipidemia, unspecified
- E78.6 Lipoprotein deficiency
- Abetalipoproteinemia
- Depressed HDL cholesterol
- High-density lipoprotein deficiency
- Hypoalphalipoproteinemia
- Hypobetalipoproteinemia (familial)
- Lecithin cholesterol acyltransferase deficiency
- Tangier disease
- E78.7 Disorders of bile acid and cholesterol metabolism
- Excludes1: Niemann-Pick disease type C (E75.242)
- E78.70 Disorder of bile acid and cholesterol metabolism, unspecified
- E78.71 Barth syndrome
- E78.72 Smith-Lemli-Opitz syndrome
- E78.79 Other disorders of bile acid and cholesterol metabolism
- E78.8 Other disorders of lipoprotein metabolism
- E78.81 Lipoid dermatoarthritis
- E78.89 Other lipoprotein metabolism disorders
- E78.9 Disorder of lipoprotein metabolism, unspecified
E79 Disorders of purine and pyrimidine metabolism
edit- Excludes1: Ataxia-telangiectasia (Q87.1)
- Bloom's syndrome (Q82.8)
- Cockayne's syndrome (Q87.1)
- calculus of kidney (N20.0)
- combined immunodeficiency disorders (D81.-)
- Fanconi's anemia (D61.09)
- gout ( M1a-, M10.-)
- orotaciduric anemia (D53.0)
- progeria (E34.8)
- Werner's syndrome (E34.8)
- xeroderma pigmentosum (Q82.1)
- E79.0 Hyperuricemia without signs of inflammatory arthritis and tophaceous disease
- Asymptomatic hyperuricemia
- E79.1 Lesch-Nyhan syndrome
- HGPRT deficiency
- E79.2 Myoadenylate deaminase deficiency
- E79.8 Other disorders of purine and pyrimidine metabolism
- Hereditary xanthinuria
- E79.9 Disorder of purine and pyrimidine metabolism, unspecified
E80 Disorders of porphyrin and bilirubin metabolism
edit- Includes: defects of catalase and peroxidase
- E80.0 Hereditary erythropoietic porphyria
- Congenital erythropoietic porphyria
- Erythropoietic protoporphyria
- E80.1 Porphyria cutanea tarda
- E80.2 Other and unspecified porphyria
- E80.20 Unspecified porphyria
- Porphyria NOS
- E80.21 Acute intermittent (hepatic) porphyria
- E80.29 Other porphyria
- Hereditary coproporphyria
- E80.20 Unspecified porphyria
- E80.3 Defects of catalase and peroxidase
- Acatalasia [Takahara]
- E80.4 Gilbert's syndrome
- E80.5 Crigler-Najjar syndrome
- E80.6 Other disorders of bilirubin metabolism
- Dubin-Johnson syndrome
- Rotor's syndrome
- E80.7 Disorder of bilirubin metabolism, unspecified
E83 Disorders of mineral metabolism
edit- Excludes1: dietary mineral deficiency (E58-E61)
- parathyroid disorders (E20-E21)
- vitamin D deficiency (E55.-)
- E83.0 Disorders of copper metabolism
- E83.00 Disorder of copper metabolism, unspecified
- E83.01 Wilson's disease
- Code also associated Kayser Fleischer ring (H18.04-)
- E83.09 Other disorders of copper metabolism
- Menkes' ( kinky hair) (steely hair) disease
- E83.1 Disorders of iron metabolism
- Excludes1: iron deficiency anemia (D50.-)
- sideroblastic anemia (D64.0-D64.3)
- E83.10 Disorder of iron metabolism, unspecified
- E83.11 Hemochromatosis
- E83.19 Other disorders of iron metabolism
- Excludes1: iron deficiency anemia (D50.-)
- E83.2 Disorders of zinc metabolism
- Acrodermatitis enteropathica
- E83.3 Disorders of phosphorus metabolism and phosphatases
- Excludes1: adult osteomalacia (M83.-)
- osteoporosis (M80-)
- E83.30 Disorder of phosphorus metabolism, unspecified
- E83.31 Familial hypophosphatemia
- Vitamin D-resistant osteomalacia
- Vitamin D-resistant rickets
- Excludes1: vitamin D-deficiency rickets (E55.0)
- E83.32 Hereditary vitamin D-dependent rickets (type 1) (type 2)
- 25-hydroxyvitamin D 1-alpha-hydroxylase deficiency
- Pseudovitamin D deficiency
- Vitamin D receptor defect
- E83.39 Other disorders of phosphorus metabolism
- Acid phosphatase deficiency
- Hypophosphatasia
- Excludes1: adult osteomalacia (M83.-)
- E83.4 Disorders of magnesium metabolism
- E83.40 Disorders of magnesium metabolism, unspecified
- E83.41 Hypermagnesemia
- E83.42 Hypomagnesemia
- E83.49 Other disorders of magnesium metabolism
- E83.5 Disorders of calcium metabolism
- Excludes1: chondrocalcinosis (M11.1-M11.2)
- hungry bone syndrome (E83.81)
- hyperparathyroidism (E21.0-E21.3)
- E83.50 Unspecified disorder of calcium metabolism
- E83.51 Hypocalcemia
- E83.52 Hypercalcemia
- Familial hypocalciuric hypercalcemia
- E83.59 Other disorders of calcium metabolism
- Idiopathic hypercalciuria
- E83.8 Other disorders of mineral metabolism
- E83.81 Hungry bone syndrome
- E83.89 Other disorders of mineral metabolism
- E83.9 Disorder of mineral metabolism, unspecified
E84 Cystic fibrosis
edit- Includes: mucoviscidosis
- E84. 0 Cystic fibrosis with pulmonary manifestations
- Use additional code to identify any infectious organism present, such as:
- Pseudomonas (B96.5)
- E84.1 Cystic fibrosis with intestinal manifestations
- E84.11 Meconium ileus in cystic fibrosis
- Excludes1: meconium ileus not due to cystic fibrosis (P76.0)
- E84.19 Cystic fibrosis with other intestinal manifestations
- Distal intestinal obstruction syndrome
- E84.11 Meconium ileus in cystic fibrosis
- E84.8 Cystic fibrosis with other manifestations
- E84.9 Cystic fibrosis, unspecified
E85 Amyloidosis
edit- Excludes1: Alzheimer's disease (G30.0-)
- E85.0 Non-neuropathic heredofamilial amyloidosis
- Familial Mediterranean fever
- Hereditary amyloid nephropathy
- E85.1 Neuropathic heredofamilial amyloidosis
- Amyloid polyneuropathy (Portuguese)
- E85.2 Heredofamilial amyloidosis, unspecified
- E85.3 Secondary systemic amyloidosis
- Hemodialysis-associated amyloidosis
- E85.4 Organ-limited amyloidosis
- Localized amyloidosis
- E85.8 Other amyloidosis
- E85.9 Amyloidosis, unspecified
E86 Volume depletion
edit- Excludes1: dehydration of newborn (P74.1)
- hypovolemic shock NOS (R57.1)
- postprocedural hypovolemic shock (T81.1)
- traumatic hypovolemic shock (T79.4)
- E86.0 Dehydration
- E86.1 Hypovolemia
- Depletion of volume of plasma
- E86.9 Volume depletion, unspecified
E87 Other disorders of fluid, electrolyte and acid-base balance
edit- Excludes1: diabetes insipidus (E23.2)
- electrolyte imbalance associated with hyperemesis gravidarum (O21.1)
- electrolyte imbalance following ectopic or molar pregnancy (O08.5)
- familial periodic paralysis (G72.3)
- E87.0 Hyperosmolality and hypernatremia
- Sodium [Na] excess
- Sodium [Na] overload
- E87.1 Hypo-osmolality and hyponatremia
- Sodium [Na] deficiency
- Excludes1: syndrome of inappropriate secretion of antidiuretic hormone (E22.2)
- E87.2 Acidosis
- Acidosis NOS
- Lactic acidosis
- Metabolic acidosis
- Respiratory acidosis
- Excludes1: diabetic acidosis - see categories E10-E13 with ketoacidosis
- E87.3 Alkalosis
- Alkalosis NOS
- Metabolic alkalosis
- Respiratory alkalosis
- E87.4 Mixed disorder of acid-base balance
- E87.5 Hyperkalemia
- Potassium [K] excess
- Potassium [K] overload
- E87.6 Hypokalemia
- Potassium [K] deficiency
- E87.7 Fluid overload
- Excludes1: edema NOS (R60.-)
- E87.8 Other disorders of electrolyte and fluid balance, not elsewhere classified
- Electrolyte imbalance NOS
- Hyperchloremia
- Hypochloremia
E88 Other and unspecified metabolic disorders
edit- Use additional codes for associated conditions
- Excludes1: histiocytosis X (chronic) (C96.6)
- E88.0 Disorders of plasma-protein metabolism, not elsewhere classified
- Excludes1: disorder of lipoprotein metabolism (E78.-)
- monoclonal gammopathy (of undetermined significance) (D47.2)
- polyclonal hypergammaglobulinemia (D89.0)
- Waldenström macroglobulinemia (C88.0)
- E88.01 Alpha-1-antitrypsin deficiency
- AAT deficiency
- E88.09 Other disorders of plasma-protein metabolism, not elsewhere classified
- Bisalbuminemia
- Excludes1: disorder of lipoprotein metabolism (E78.-)
- E88.1 Lipodystrophy, not elsewhere classified
- Lipodystrophy NOS
- Excludes1: Whipple's disease (K90.81)
- E88.2 Lipomatosis, not elsewhere classified
- Lipomatosis NOS
- Lipomatosis (Check) dolorosa [Dercum]
- E88. 3 Tumor lysis syndrome
- Tumor lysis syndrome (spontaneous)
- Tumor lysis syndrome following antineoplastic drug chemotherapy
- Code first (T45.1-) to identify drug, if drug induced
- E88.4 Mitochondrial metabolism disorders
- Excludes1: disorders of pyruvate metabolism (E74.4)
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.22)
- Leigh's encephalopathy (G31.82)
- Mitochondrial myopathy, NEC (G71.3)
- Reye's syndrome (G93.7)
- E88.40 Mitochondrial metabolism disorder, unspecified
- E88.41 MELAS syndrome
- Mitochondrial myopathy, encephalopathy, lactic acidosis and stroke-like episodes
- E88.42 MERRF syndrome
- Myoclonic epilepsy associated with ragged-red fibers
- Code also: myoclonic epilepsy (G40.3-)
- E88.49 Other mitochondrial metabolism disorders
- Excludes1: disorders of pyruvate metabolism (E74.4)
- E88.8 Other specified metabolic disorders
- E88.81 Metabolic syndrome
- Dysmetabolic syndrome X
- E88.89 Other specified metabolic disorders
- Launois-Bensaude adenolipomatosis
- E88.81 Metabolic syndrome
- E88.9 Metabolic disorder, unspecified
E89 Postprocedural endocrine and metabolic complications and disorders, not elsewhere classified
edit- Excludes2: intraoperative complications of endocrine system organ or structure (E36.0-, E36.1-, E36.8)
- E89.0 Postprocedural hypothyroidism
- Postirradiation hypothyroidism
- Postsurgical hypothyroidism
- E89.1 Postprocedural hypoinsulinemia
- Postpancreatectomy hyperglycemia
- Postsurgical hypoinsulinemia
- Use additional code, if applicable, to identify:
- acquired absence of pancreas (Z90.89)
- diabetes mellitus (E11.-)
- insulin use (Z79.4)
- Excludes1: transient postprocedural hyperglycemia (R73.9)
- transient postprocedural hypoglycemia (E16.2)
- E89.2 Postprocedural hypoparathyroidism
- Parathyroprival tetany
- E89.3 Postprocedural hypopituitarism
- Postirradiation hypopituitarism
- E89. 4 Postprocedural ovarian failure
- E89.40 Asymptomatic postprocedural ovarian failure
- Postprocedural ovarian failure NOS
- E89.41 Symptomatic postprocedural ovarian failure
- Symptoms such as flushing, sleeplessness, headache, lack of concentration, associated with postprocedural menopause
- E89.40 Asymptomatic postprocedural ovarian failure
- E89.5 Postprocedural testicular hypofunction
- E89.6 Postprocedural adrenocortical (-medullary) hypofunction
- E89.8 Other postprocedural endocrine and metabolic complications and disorders
- E89.81 Postprocedural hemorrhage and hematoma of an endocrine system organ or structure following a procedure
- E89.810 Postprocedural hemorrhage and hematoma of an endocrine system organ or structure following an endocrine system procedure
- E89.811 Postprocedural hemorrhage and hematoma of an endocrine system organ or structure following other procedure
- E89.89 Other postprocedural endocrine and metabolic complications and disorders
- Use additional code, if applicable, to further specify disorder
- E89.81 Postprocedural hemorrhage and hematoma of an endocrine system organ or structure following a procedure